Abstract |
Tracheal agenesis (TA) is an extremely rare, typically fatal congenital tracheal malformation. Lack of prenatal symptoms and emergent presentation usually lead to a failure to arrive at the correct diagnosis and manage the airway properly before the onset of irreversible cerebral anoxia. Esophageal atresia (EA) encompasses a group of congenital anomalies comprising an interruption of the continuity of the esophagus with or without a persistent communication with the trachea. In 86% of cases, there is a distal tracheoesophageal fistula (TEF); in 7%, there is no fistulous connection, whereas in 4%, there is a TEF without atresia. We report the case of an infant born with TA and EA with proximal and distal bronchoesophageal fistulas. During 3 consecutive antenatal ultrasound examinations, there had been polyhydramniosis, difficulty visualizing the stomach, and dilatation of proximal esophagus, leading to a presumptive diagnosis of EA. The clinical presentation, embryology, classification, and surgical management are discussed.
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Authors | Mehmet Demircan, Tugrul Aksoy, Canan Ceran, Ayse Kafkasli |
Journal | Journal of pediatric surgery
(J Pediatr Surg)
Vol. 43
Issue 8
Pg. e1-3
(Aug 2008)
ISSN: 1531-5037 [Electronic] United States |
PMID | 18675618
(Publication Type: Case Reports, Journal Article)
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Topics |
- Abnormalities, Multiple
(diagnosis, surgery)
- Bronchial Fistula
(diagnosis, surgery)
- Esophageal Atresia
(diagnosis, surgery)
- Esophageal Fistula
(diagnosis, surgery)
- Fatal Outcome
- Heart Arrest
(therapy)
- Humans
- Infant, Newborn
- Intraoperative Complications
(diagnosis, therapy)
- Male
- Risk Assessment
- Trachea
(abnormalities)
- Tracheal Diseases
(congenital, surgery)
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