Dentinogenesis imperfecta: a case report.

Abstract

Dentinogenesis imperfecta is an autosomal dominant disorder of tooth development characterized by the presence of opalescent dentin, resulting in a dusky blue to brownish discoloration of the teeth. This condition is genetically and clinically heterogeneous; it may affect only the teeth or it may be associated with the osteogenesis imperfecta. Dentinogenesis imperfecta has been subdivided into three types: type I is associated with osteogenesis imperfecta; in type II there is no associated osteogenesis imperfecta; and when the condition is associated with the Brandywine triracial isolate and large pulp chambers it is classified as type III. This report describes a 16-year-old female patient who showed the characteristic dental features of dentinogenesis imperfecta type II. The etiology and prevalence of the disorder, and a comprehensive treatment plan, will be briefly reviewed.

• Authors: P Subramaniam, S Mathew, S N Sugnani
• Journal: Journal of the Indian Society of Pedodontics and Preventive Dentistry (J Indian Soc Pedod Prev Dent) Vol. 26 Issue 2 Pg. 85-7 (Jun 2008) ISSN: 0970-4388 [Print] India
• PMID: 18603736 (Publication Type: Case Reports, Journal Article)

Topics

• Adolescent
• Crowns
• Dentinogenesis Imperfecta (classification, physiopathology, therapy)
• Female
• Humans
• Patient Satisfaction
• Root Canal Therapy (methods)
• Treatment Outcome