Successful living-related liver transplantation in a child with familial yellow nail syndrome and fulminant hepatic failure: report of a case.

Abstract

An 11-yr-old boy with familial YNS and FHF and who underwent LRLT is presented. LRLT was performed from his father with YNS. The findings of hepatic failure resolved immediately after LRLT, but severe respiratory complications and chylous ascites were observed during the follow-up. At 12 months after successful LT, the patient has good graft function, but findings of YNS including chronic cough, lymphedema and yellow nails are still present. To the best of our knowledge, this is the first case of YNS who underwent LRLT for FHF.

• Authors: Zarife Kuloğlu, Gonca Ustündağ, Ceyda Tuna Kirsaçlioğlu, Aydan Kansu, Meltem Bingol-Kologlu, Rahsan Vargun, Selcuk Hazinedaroğlu, Selim Karayalçin, Nurten Girgin
• Journal: Pediatric transplantation (Pediatr Transplant) Vol. 12 Issue 8 Pg. 906-9 (Dec 2008) ISSN: 1399-3046 [Electronic] Denmark
• PMID: 18503484 (Publication Type: Case Reports, Journal Article)

Topics

• Adult
• Ascites (metabolism)
• Child
• Cough
• Family Health
• Humans
• Jaundice (complications, therapy)
• Liver Diseases (complications, therapy)
• Liver Failure (complications, therapy)
• Liver Failure, Acute (complications, therapy)
• Liver Transplantation (methods)
• Lymphedema (therapy)
• Male
• Nails (pathology)
• Syndrome