Fontan operation through a right lateral thoracotomy to treat Cantrell syndrome with severe ectopia cordis.

Abstract

A median sternotomy would be very difficult for Cantrell syndrome with severe ectopia cordis. For Cantrell syndrome and tricuspid atresia after left modified Blalock-Taussig shunt with severe ectopia cordis, defect in the middle and inferior portion of the sternum, and the closing of ventriculo-peritoneal shunt, we performed extracardiac total cavopulmonary connection through a right lateral thoracotomy after establishing right modified Blalock-Taussig shunt and performing coil embolization of left modified Blalock-Taussig shunt by cardiologists.

• Authors: Yuki Okamoto, Yorikazu Harada, Shunji Uchita
• Journal: Interactive cardiovascular and thoracic surgery (Interact Cardiovasc Thorac Surg) Vol. 7 Issue 2 Pg. 278-9 (Apr 2008) ISSN: 1569-9285 [Electronic] England
• PMID: 18203768 (Publication Type: Case Reports, Journal Article)

Topics

• Abnormalities, Multiple (physiopathology, surgery)
• Arteriovenous Shunt, Surgical
• Cardiac Catheterization
• Child
• Ectopia Cordis (complications, physiopathology, surgery)
• Embolization, Therapeutic
• Female
• Fontan Procedure
• Hemodynamics
• Hernia, Umbilical (complications, surgery)
• Humans
• Pulmonary Artery (surgery)
• Syndrome
• Thoracotomy
• Treatment Outcome
• Tricuspid Atresia (complications, physiopathology, surgery)
• Vena Cava, Inferior (surgery)
• Vena Cava, Superior (surgery)