Klippel-Feil syndrome and Sprengel deformity combined with an intraspinal course of the left subclavian artery and a bovine aortic arch variant.

Abstract

We present a case of Klippel-Feil syndrome and Sprengel deformity with a bovine aortic arch and an aberrant course of the left subclavian artery in a 14-year-old boy. CT and MR imaging of the neck and upper thorax demonstrated a cervical osseous segmentation anomaly, a left common carotid artery originating from the innominate artery, and a left subclavian artery coursing through the intraspinal space at the C6 through T1 level. Possible embryonic mechanisms and clinical significance of this variant are reviewed.

• Authors: F Floemer, O Magerkurth, C Jauckus, J Lütschg, J F Schneider
• Journal: AJNR. American journal of neuroradiology (AJNR Am J Neuroradiol) Vol. 29 Issue 2 Pg. 306-7 (Feb 2008) ISSN: 1936-959X [Electronic] United States
• PMID: 18024572 (Publication Type: Case Reports, Journal Article)

Topics

• Adolescent
• Aorta, Thoracic (abnormalities, diagnostic imaging, pathology)
• Cervical Vertebrae (abnormalities, diagnostic imaging, pathology)
• Humans
• Klippel-Feil Syndrome (diagnosis)
• Magnetic Resonance Imaging
• Male
• Scapula (abnormalities, diagnostic imaging, pathology)
• Subclavian Artery (abnormalities, diagnostic imaging, pathology)
• Tomography, X-Ray Computed