Abstract | INTRODUCTION: Central diabetes insipidus is most frequently reported to occur after a trauma from surgery or accident. However, between 30 and 50% of cases are considered idiopathic. It's a rare complication of myelodysplastic syndrome. CASE REPORT: A 61-year-old patient presented central diabetes insipidus revealing, 17 months before, chronic myelomonocytic leukemia. Cytogenetics studies revealed monosomy 7. Acute myeloid leukemia appears 3 months after training rapid patient's death. DISCUSSION: Blood examination is necessary before to conclude idiopathic central diabetes insipidus. The discovery of chronic myelomonocytic leukemia implicates a rapid managing before its possible acute myeloid leukemia transformation. Indeed, prognosis of central diabetes insipidus and acute myeloid leukemia associated, in presence of monosomy 7, is very poor.
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Authors | B Graffin, P Bernard, C Landais, O Gisserot, M Aletti, G Leyral, J-F Paris, P Carli |
Journal | La Revue de medecine interne
(Rev Med Interne)
Vol. 28
Issue 10
Pg. 698-700
(Oct 2007)
ISSN: 0248-8663 [Print] France |
Vernacular Title | Diabète insipide central inaugural d'une leucémie myélomonocytaire chronique. |
PMID | 17850929
(Publication Type: Case Reports, English Abstract, Journal Article)
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Topics |
- Chromosomes, Human, Pair 7
(genetics)
- Diabetes Insipidus
(diagnosis)
- Diagnosis, Differential
- Fatal Outcome
- Humans
- Leukemia, Myeloid, Acute
(diagnosis)
- Leukemia, Myelomonocytic, Chronic
(diagnosis)
- Male
- Middle Aged
- Monosomy
(diagnosis, genetics)
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