Authors | R J Wanders, C W van Roermund, C Jakobs, H J ten Brink |
Journal | Journal of inherited metabolic disease
(J Inherit Metab Dis)
Vol. 14
Issue 3
Pg. 349-52
( 1991)
ISSN: 0141-8955 [Print] United States |
PMID | 1770789
(Publication Type: Journal Article)
|
Chemical References |
- Phytanic Acid
- Oxidoreductases
- pristanoyl-CoA oxidase
|
Topics |
- Centrifugation, Density Gradient
- Decarboxylation
- Humans
- Microbodies
(enzymology, metabolism)
- Mitochondria, Liver
(enzymology, metabolism)
- Oxidoreductases
(analysis)
- Phytanic Acid
(metabolism)
- Zellweger Syndrome
(enzymology, metabolism)
|