[Recurrence of thromboembolic disease after splenectomy for hereditary xerocytosis].

Abstract

CASE REPORT:

The diagnosis of hereditary xerocytosis is made in a 57 year old woman splenectomized 30 years ago for a chronic hemolytic anemia. In following, she developed many thrombophlebitis of lower limbs and portal vein.

DISCUSSION:

The methods of diagnosis of this rare hereditary stomatocytosis are recalled, and the mechanisms of thrombotic tendency after splenectomy are discussed. This case underlines the fact that splenectomy is banned in the treatment of hereditary stomatocytosis, and that the serious consequences of iron overload, which is very frequent in this disease, must be prevented.

• Authors: P Carli, B Graffin, O Gisserot, C Landais, J-P De Jaureguiberry
• Journal: La Revue de medecine interne (Rev Med Interne) Vol. 28 Issue 12 Pg. 879-81 (Dec 2007) ISSN: 0248-8663 [Print] France
• Vernacular Title: Maladie thromboembolique récidivante après splénectomie pour stomatocytose héréditaire.
• PMID: 17590481 (Publication Type: Case Reports, English Abstract, Journal Article)

Topics

• Anemia, Hemolytic, Congenital (surgery)
• Female
• Humans
• Iron Overload (complications)
• Middle Aged
• Recurrence
• Splenectomy