Abstract | INTRODUCTION:
Gingival fibromatosis is an inherited disease of the gingival tissue causing proliferative fibrous lesions occurring alone or as one feature of a more widespread syndrome. OBSERVATION: DISCUSSION:
Gingival fibromatosis is a rare condition characterized by a gingival hypertrophy. It is transmitted by autosomal dominant or recessive inheritance. The oral examination and histology provides the diagnosis. The treatment consistes of surgical removal of the hyperplasic fibrous tissue. Prognosis is dominated by the risk of recurrence which is frequent. Generally, gingival fibromatosis is isolated. In rare cases, it can be associated with symptoms sugges- ting a syndromic diagnosis such as Zimmermann Laband syndrome. In addition to gingival hypertrophy, skeletal anomalies can involve the fingers, the toenails, the thorax or the vertebrae. Splenomegaly and joint hyperextensibility can also be found.
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Authors | L Kissi, I Benyahya, A Rifki |
Journal | Revue de stomatologie et de chirurgie maxillo-faciale
(Rev Stomatol Chir Maxillofac)
Vol. 107
Issue 6
Pg. 477-80
(Dec 2006)
ISSN: 0035-1768 [Print] France |
Vernacular Title | Fibromatose gingivale dans le cadre d'une atteinte syndromique. |
PMID | 17195004
(Publication Type: Case Reports, English Abstract, Journal Article)
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Topics |
- Adult
- Female
- Fibromatosis, Gingival
(surgery)
- Heart Defects, Congenital
- Hemostatic Techniques
(instrumentation)
- Humans
- Lip
(abnormalities)
- Musculoskeletal Abnormalities
- Nails, Malformed
- Nose
(abnormalities)
- Syndrome
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