[The use of Nd-Yag laser in the treatment of tracheal tumor in 14 years old child with mukopolisacharydosis type II].

Abstract

Hunter's Syndrome (MPS II) is a class of hereditary disorder characterized by a deficiency of specific enzyme--iduronate sulphatase required to break down mucopolisacharides and occurs in Poland in one of 100-150 thousand male live births. MPS II may be lethal in the second decade of life as a result of infiltrativ cardiomiopathy leading to irreversible heart failure or upper airway obstruction caused by infiltration, granulation and deformation in trachea or larynx. We report a case of 14-year-old male with Hunter Syndrome who developed tracheal obstruction and was treated with Nd-Yag laser. We discuss the possibility of treatment and our results--improvement in patient's symptomatic and functional status.

• Authors: Józef Mierzwiński, Aleksander Zwierz, Artur Jaworski, Ryszard Redziński, Władysław Bandrowicz, Krzysztof Dalke, Paweł Burduk
• Journal: Otolaryngologia polska = The Polish otolaryngology (Otolaryngol Pol) Vol. 60 Issue 4 Pg. 603-6 ( 2006) ISSN: 0030-6657 [Print] Poland
• Vernacular Title: Zastosowanie lasera Nd-Yag w leczeniu guza tchawicy w przebiegu mukopolisacharydozy u dziecka.
• PMID: 17152817 (Publication Type: Case Reports, English Abstract, Journal Article)

Chemical References

• Neodymium

Topics

• Adolescent
• Airway Obstruction (diagnosis, etiology, surgery)
• Bronchoscopy
• Humans
• Laser Therapy
• Male
• Mucopolysaccharidosis II (complications)
• Neodymium
• Tracheal Neoplasms (diagnosis, etiology, surgery)
• Treatment Outcome