| Abstract | Hyper-IgD and periodic fever syndrome (HIDS) is a hereditary autoinflammatory syndrome, characterized by recurrent inflammatory attacks. Treatment of HIDS is difficult. Recently, the IL-1ra analogue anakinra was reported to be successful in aborting the IgD inflammatory attacks in a vaccination model. We report a clinical case of spectacular reduction of febrile attacks in a severe HIDS patient. |
| Authors | M Cailliez, F Garaix, C Rousset-Rouvière, D Bruno, I Kone-Paut, J Sarles, B Chabrol, M Tsimaratos
(Affiliation: AP-HM Timone-Enfants, F-13385, Marseilles Cedex 05, France.)
|
| Journal | Journal of inherited metabolic disease
(J Inherit Metab Dis)
Vol. 29
Issue 6
Pg. 763
(Dec 2006)
ISSN: 1573-2665 [Electronic] Netherlands |
| PMID | 17103011
(Publication Type: Case Reports, Journal Article)
|
| Chemical References |
- Immunoglobulin D
- Interleukin 1 Receptor Antagonist Protein
|
| Topics |
- Fever
(etiology, therapy)
- Humans
- Hypergammaglobulinemia
(complications, therapy)
- Immunoglobulin D
(chemistry)
- Inflammation
- Interleukin 1 Receptor Antagonist Protein
(therapeutic use)
- Syndrome
|