Anesthesia in a child with fibrodysplasia ossificans progressiva.

Abstract

We describe the anesthesia management of a 12-year-old girl, diagnosed with fibrodysplasia ossificans progressiva (FOP), who presented with a submandibular abscess. FOP is a rare, inherited disorder with heterotopic bone formation and progressive musculoskeletal disability. This disability ultimately confines patients to a wheelchair. Minor trauma following dental treatment may lead to ankylosis of the jaw. Subsequent to this disability, which resulted in poor dental hygiene, our patient developed a dental abscess. This spread along the mandibular margin and under the tongue. She presented with an impending airway compromise in an already difficult situation. The options for airway management in a child with limited mouth opening are discussed.

• Authors: Rita Vashisht, Dylan Prosser
• Journal: Paediatric anaesthesia (Paediatr Anaesth) Vol. 16 Issue 6 Pg. 684-8 (Jun 2006) ISSN: 1155-5645 [Print] France
• PMID: 16719887 (Publication Type: Case Reports, Journal Article)

Topics

• Ambulatory Surgical Procedures
• Anesthesia (methods)
• Child
• Female
• Humans
• Intubation, Intratracheal (methods)
• Mandible (surgery)
• Myositis Ossificans (complications)