Klippel-Trenaunay syndrome with small vessel pulmonary arterial hypertension.

Abstract

A patient with Klippel-Trenaunay syndrome and pulmonary arterial hypertension not associated with chronic thrombo-embolic pulmonary hypertension is described. It is hypothesised that pulmonary arterial hypertension is another complication associated with the Klippel-Trenaunay syndrome, possibly due to haemodynamic changes of small vessel abnormalities.

• Authors: S Ulrich, M Fischler, B Walder, T Pfammatter, R Speich
• Journal: Thorax (Thorax) Vol. 60 Issue 11 Pg. 971-3 (Nov 2005) ISSN: 0040-6376 [Print] England
• PMID: 16263952 (Publication Type: Case Reports, Journal Article)

Topics

• Humans
• Hypertension, Pulmonary (etiology)
• Klippel-Trenaunay-Weber Syndrome (complications)
• Male
• Microcirculation
• Middle Aged
• Pulmonary Embolism (etiology)