Abstract | UNLABELLED: Cutis marmorata telangiectatica congenita (CMTC) is an uncommon sporadic congenital vascular anomaly characterised by persistent cutis marmorata, telangiectasia, and phlebectasia. The disease usually has a benign clinical course and over 50% of cases recover spontaneously without specific treatment. The occurrence of life-threatening complications in CMTC is rare. CONCLUSION: We report a neonate with life-threatening cutis marmorata telangiectatica congenita which was complicated by gangrenous ulceration, bleeding episodes, and hypovolaemic shock.
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Authors | I-Jan Hu, Ming-Ting Chen, Hao-Chih Tai, Po-Nien Tsao, Hung-Chieh Chou, Wu-Shiun Hsieh |
Journal | European journal of pediatrics
(Eur J Pediatr)
Vol. 164
Issue 7
Pg. 411-3
(Jul 2005)
ISSN: 0340-6199 [Print] Germany |
PMID | 15812662
(Publication Type: Case Reports, Journal Article)
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Topics |
- Capillaries
(pathology)
- Dilatation, Pathologic
- Female
- Gangrene
- Humans
- Infant, Newborn
- Shock
- Skin Diseases
(complications, physiopathology)
- Skin Ulcer
(pathology, therapy)
- Telangiectasis
(complications, physiopathology)
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