Abstract | STUDY DESIGN: OBJECTIVES: Our objectives were as follows: to describe the previously unreported findings of posterior element autofusion and ligamentum flavum ossification; to increase surgeon awareness to the nature of this condition and associated findings; and to prepare the surgeons for the possibility of autofusion and the required surgical modifications, including extensive osteotomies at the time of spinal fusion surgery to achieve correction based on these findings. SUMMARY OF BACKGROUND DATA: METHODS: RESULTS: The spinal deformities associated with central core disease in these 2 cases were severe. The posterior elements underwent autofusion necessitating alteration in surgical technique to correct the deformity. Despite the risks of malignant hyperthermia and the difficulty of surgical correction, good clinical improvements can be achieved even in cases of severe deformity. CONCLUSIONS: A diagnosis of central core disease must be considered in patients presenting with severe spinal deformity and myopathic symptoms. This spinal deformity may be progressive and become severe. Surgical intervention in these cases may be complicated by posterior element autofusion necessitating alteration in surgical technique to correct the deformity. Despite the risk of malignant hyperthermia, surgery may be performed safely.
|
Authors | Anthony M Sestero, Joseph H Perra |
Journal | Spine
(Spine (Phila Pa 1976))
Vol. 30
Issue 2
Pg. E50-5
(Jan 15 2005)
ISSN: 1528-1159 [Electronic] United States |
PMID | 15644748
(Publication Type: Case Reports, Journal Article)
|
Topics |
- Adolescent
- Calcinosis
(pathology)
- Female
- Humans
- Kyphosis
(diagnosis, etiology, surgery)
- Ligamentum Flavum
(pathology)
- Male
- Malignant Hyperthermia
- Myopathy, Central Core
(complications, diagnosis, surgery)
- Scoliosis
(etiology, pathology, surgery)
- Spinal Fusion
(methods)
- Spine
(pathology, surgery)
- Treatment Outcome
- Zygapophyseal Joint
(pathology)
|