[Classification of vascular anomalies (tumours and malformations). Clinical characteristics and natural history].

Abstract

Vascular anomalies are divided into tumours and malformations. Haemangiomas are the most frequent amongst the former. Not normally present at birth, except in a premonitory form, they grow for 10-12 months due to hyperplasia, to subsequently undergo a progressive involution for a period that might last from ten to twelve years. They have an incidence of up to 12% in newborns; they are more common amongst girls; and are divided into superficial, deep and compound. Congenital haemangiomas and those that do not undergo involution are considered to be rare entities. Vascular malformations, with a lower incidence than haemangiomas, are always present at birth, they grow by hypertrophy and never undergo involution. According to the classification of the ISSVA, vascular malformations are divided - depending on the vessel affected - into capillary or venular (port-wine stain), venous, lymphatic, arteriovenous and combined or complex. Each of these has certain defining clinical and haemodynamic peculiarities. Within the final group are included some with a low flow, such as the Klippel-Trenaunay syndrome (venous and lymphatic venular vascular malformation associated with the muscular-skeletal hypertrophy of an extremity), and others with a high flow, such as the Parkes-Weber syndrome.

• Authors: P Redondo
• Journal: Anales del sistema sanitario de Navarra (An Sist Sanit Navar) Vol. 27 Suppl 1 Pg. 9-25 ( 2004) ISSN: 1137-6627 [Print] Spain
• Vernacular Title: Clasificación de las anomalías vasculares (tumores y malformaciones). Características clínicas e historia natural.
• PMID: 15148508 (Publication Type: English Abstract, Journal Article, Review)

Topics

• Arteriovenous Malformations (classification, diagnosis)
• Blood Vessels (abnormalities)
• Hemangioma (classification, congenital, diagnosis)
• Humans
• Lymphatic Diseases (classification, diagnosis)
• Neoplasms, Vascular Tissue (classification, congenital, diagnosis)