Left-sided facial nevus with contralateral leptomeningeal angiomatosis in a child with Sturge-Weber syndrome: case report.

Abstract

Sturge-Weber syndrome is characterized by a facial vascular nevus associated with an ipsilateral leptomeningeal angioma. Variants of this classical presentation have been described in the literature, some of which have prognostic significance. We report a magnetic resonance imaging (MRI)-confirmed variant of a leptomeningeal angioma contralateral to the facial nevus. We describe one patient with Sturge-Weber syndrome who presented with a left-sided facial nevus, left eye glaucoma, episodes of left-sided weakness, and right-sided leptomeningeal angiomatosis by gadolinium-enhanced brain MRI. The literature regarding variants of Sturge-Weber syndrome and their prognosis is reviewed. The prognosis for this variant is likely similar to Sturge-Weber syndrome with an ipsilateral leptomeningeal angioma.

• Authors: Peter Widdess-Walsh, Neil Roy Friedman
• Journal: Journal of child neurology (J Child Neurol) Vol. 18 Issue 4 Pg. 304-5 (Apr 2003) ISSN: 0883-0738 [Print] United States
• PMID: 12760437 (Publication Type: Case Reports, Journal Article)

Topics

• Adolescent
• Angiomatosis (etiology, pathology)
• Facial Neoplasms (etiology, pathology)
• Female
• Humans
• Magnetic Resonance Imaging
• Meningeal Neoplasms (etiology, pathology)
• Nevus (etiology, pathology)
• Skin Neoplasms (etiology, pathology)
• Sturge-Weber Syndrome (complications, pathology)