Total hip arthroplasty for a patient with angel-shaped phalango-epiphyseal dysplasia (ASPED). A case report.

Abstract

Angel-shaped phalango-epiphyseal dysplasia is characterized by the angel shape of the middle phalanx and severe coxarthrosis in adult life. This osteochondrodysplasia shows a further variety of heterogeneous multiple epiphyseal dysplasias. It also shows a late and dysplastic development of the femoral head that leads to osteoarthrotic changes with severe hip pain and gait disturbance. In this report, we show a 35-year-old female with Angel-shaped phalango-epiphyseal dysplasia that was treated by bilateral total hip arthroplasty. She has suffered from her coxalgia since she was 27 and since the age of 30 has been able to walk with the aid of crutches. The radiographs of her bilateral hip showed severe osteochondrotic changes with a progressive disappearance of the joint space. Total hip arthroplasties were performed to treat the osteoarthrosis on the bilateral hip joint due to Angel-shaped phalango-epiphyseal dysplasia. One year after surgery, she is pain-free, and able to walk with a cane. Based on this case, we propose that total hip arthroplasty should be considered one of the treatments for the coxopathy in patients with Angel-shaped phalangoepiphyseal dysplasia.

• Authors: Hideki Warashina, Sinji Sakano, Sinji Kitamura, Ken-ichi Yamauchi, Hiroshi Kito, Yukiharu Hasegawa
• Journal: Nagoya journal of medical science (Nagoya J Med Sci) Vol. 65 Issue 3-4 Pg. 103-7 (Nov 2002) ISSN: 0027-7622 [Print] Japan
• PMID: 12580536 (Publication Type: Case Reports, Journal Article)

Topics

• Adult
• Arthroplasty, Replacement, Hip
• Female
• Hip Dislocation, Congenital (diagnostic imaging, genetics, surgery)
• Humans
• Osteochondrodysplasias (diagnostic imaging, genetics, surgery)
• Radiography