Laryngeal neurofibroma: case report of a child.

Abstract

Neurofibromatosis is characterized by multiple café-au-lait spots and cutaneous neurofibromas. Laryngeal involvement in neurofibromatosis is rare and is usually manifested by obstructive airway symptoms. We encountered a 1 year 8-month-old girl who was a victim of neurofibromatosis with the presentation of stridor. Fiberoptic laryngoscopy revealed a round smooth mass over the right aryepiglottic fold which prolapsed into the larynx during inspiration. Carbon dioxide laser excision was performed and histopathologic examination revealed a plexiform neurofibroma. The patient had regular follow up for almost 4 years. Even though there seemed to be a recurrence, she remained symptom free.

• Authors: Yu-Chun Chen, Kuo-Sheng Lee, Cheng-Chien Yang, Ke-Chang Chang
• Journal: International journal of pediatric otorhinolaryngology (Int J Pediatr Otorhinolaryngol) Vol. 65 Issue 2 Pg. 167-70 (Sep 02 2002) ISSN: 0165-5876 [Print] Ireland
• PMID: 12176190 (Publication Type: Case Reports, Journal Article)
• Copyright: Copyright 2002 Elsevier Science Ireland Ltd.

Topics

• Biopsy, Needle
• Child, Preschool
• Female
• Follow-Up Studies
• Humans
• Immunohistochemistry
• Laparoscopy (methods)
• Laryngeal Neoplasms (diagnosis, surgery)
• Laryngoscopy (methods)
• Neurofibromatosis 1 (diagnosis, surgery)
• Risk Assessment
• Treatment Outcome