Living related kidney transplantation in a 15-year-old patient with type I hyperoxaluria: a case report.

Abstract

The following is a case report of a patient with type I hyperoxaluria who received a living related renal transplant for end-stage renal disease. The deficiency or complete absence of the hepatic enzyme alanine glyoxalate aminotransferase characterizes type I hyperoxaluria. When deficient, an overproduction of oxalate occurs, which then can be deposited in multiple end-organ systems. When performing surgery on a patient with type I hyperoxaluria, the anesthetist needs to be aware that these patients can have a host of problems ranging from cardiovascular anomalies to end-stage renal disease. A careful assessment of each system needs to be performed, along with vigilant planning of the anesthetic regimen. Through proper planning and implementation, a safe and effective anesthetic usually can be performed.

• Authors: Jeffrey W Weir, Jerry Ciancione, John O'Donnell
• Journal: AANA journal (AANA J) Vol. 70 Issue 2 Pg. 107-9 (Apr 2002) ISSN: 0094-6354 [Print] United States
• PMID: 11969060 (Publication Type: Case Reports, Journal Article)

Topics

• Adolescent
• Humans
• Hyperoxaluria, Primary (surgery)
• Kidney Transplantation
• Living Donors
• Male
• Nurse Anesthetists