[Acute bulbar palsy due to myelomeningocele and Chiari II malformation].

Abstract

We describe a case of a 10-year-old girl with myelomeningocele and type II Chiari malformation. She presented with an acute bulbar palsy requiring mechanical ventilation. Surgical decompression of the brainstem was performed and, because of a phrenic nerve palsy, surgical plication of the right diaphragm was also required. The patient s evolution was favourable. We discuss the various forms of clinical presentation of this pathology as well as its management. The importance of early diagnosis and surgical correction are also stressed as a key factor for favourable evolution.

• Authors: E Ulloa Santamaría, V Cifuentes Sabio, I Ibarra de la Rosa, M J Velasco Jabalquinto, M Frías Pérez, C Montero Schiemann, J L Pérez Navero
• Journal: Anales espanoles de pediatria (An Esp Pediatr) Vol. 52 Issue 4 Pg. 406-8 (Apr 2000) ISSN: 0302-4342 [Print] Spain
• Vernacular Title: Parálisis bulbar aguda en un caso de mielomeningocele y malformación de Chiari tipo II.
• PMID: 11003939 (Publication Type: Case Reports, English Abstract, Journal Article)

Topics

• Acute Disease
• Arnold-Chiari Malformation (complications)
• Bulbar Palsy, Progressive (etiology)
• Child
• Female
• Humans
• Meningomyelocele (complications)