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Pentalogy of Cantrell

Rare congenital deformity syndrome characterized by a combination of five anomalies as a result of neural tube defect. The five anomalies are a midline supraumbilical abdominal wall defect (e.g., OMPHALOCELE), a lower STERNUM defect, a congenital intracardiac defect, an anterior DIAPHRAGM defect, and a diaphragmatic PERICARDIUM defect (e.g., PERICARDIAL EFFUSION). Variants with incomplete and variable combinations of the defects are known. ECTOPIA CORDIS; CLEFT LIP; and CLEFT PALATE are often associated with the syndrome.
Also Known As:
Cantrell's Pentalogy; Cantrells Pentalogy; Pentalogy, Cantrell; Pentalogy, Cantrell's; Thoracoabdominal Syndromes; Cantrell Haller Ravitch syndrome; Cantrell Pentalogy; Thoracoabdominal Syndrome
Networked: 17 relevant articles (0 outcomes, 0 trials/studies)

Disease Context: Research Results

Related Diseases

1. Ectopia Cordis
2. Pulmonary Valve Stenosis (Pulmonary Stenosis)
3. Umbilical Hernia (Omphalocele)
4. Congenital Heart Defects (Congenital Heart Defect)
5. Sepsis (Septicemia)

Experts

1. McMahon, Colin J: 2 articles (12/2013 - 05/2009)
2. Ivy, Margaret P: 1 article (01/2021)
3. Morgan, Gareth J: 1 article (01/2021)
4. Zablah, Jenny E: 1 article (01/2021)
5. Kamei, Naoya: 1 article (12/2020)
6. Kubo, Shingo: 1 article (12/2020)
7. Tanaka, Toshikatsu: 1 article (12/2020)
8. Asai, Hidetsugu: 1 article (01/2020)
9. Ito, Nagomi: 1 article (01/2020)
10. Shingu, Yasushige: 1 article (01/2020)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Pentalogy of Cantrell:
1. Retinal DehydrogenaseIBA
2. Transforming Growth Factor beta (TGF-beta)IBA
3. Tretinoin (Retinoic Acid)FDA LinkGeneric
4. TitaniumIBA
5. Glucose (Dextrose)FDA LinkGeneric
6. EnzymesIBA
7. Anesthetics (Anesthetic Agents)IBA
8. Polylactic Acid-Polyglycolic Acid CopolymerIBA
9. PermacolIBA
10. A 19IBA

Therapies and Procedures

1. Blalock-Taussig Procedure
2. Norwood Procedures
3. Catheters
4. Stents
5. Punctures