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Hereditary Angioedema Type III

A form of hereditary angioedema that occurs in women and is precipitated or worsened by high ESTROGEN levels. It is associated with mutations in the gene for FACTOR XII that result in its increased activity.
Also Known As:
Angioedema, Hereditary, Type III; Angioneurotic Edema, Hereditary, with Normal C1 Inhibitor Concentration and Function; Estrogen-Related HAE; Estrogen-Sensitive HAE; Estrogen-Sensitive Hereditary Angioedema; HAE with Normal C1 Inhibitor Concentration and Function; Hereditary Angioedema with Normal C1 Inhibitor Activity; Angioedema, Estrogen-Sensitive Hereditary; Angioedemas, Estrogen-Sensitive Hereditary; Estrogen Related HAE; Estrogen Sensitive HAE; Estrogen Sensitive Hereditary Angioedema; Estrogen-Related HAEs; Estrogen-Sensitive HAEs; Estrogen-Sensitive Hereditary Angioedemas; HAE, Estrogen-Related; HAE, Estrogen-Sensitive; HAEs, Estrogen-Related; HAEs, Estrogen-Sensitive; Hereditary Angioedema, Estrogen-Sensitive; Hereditary Angioedemas, Estrogen-Sensitive
Networked: 12 relevant articles (0 outcomes, 0 trials/studies)

Disease Context: Research Results

Related Diseases

1. Angioedema
2. Hereditary Angioedema Types I and II
3. Hereditary Angioedemas
4. Urticaria (Hives)
5. Acquired angioedema

Experts

1. Bork, Konrad: 4 articles (12/2006 - 03/2003)
2. Drouet, Christian: 3 articles (08/2015 - 12/2006)
3. Nöthen, Markus M: 2 articles (08/2015 - 12/2006)
4. Renné, Thomas: 2 articles (08/2015 - 12/2006)
5. Prieto, A: 2 articles (07/2011 - 02/2009)
6. Rubio, M: 2 articles (07/2011 - 02/2009)
7. Dewald, Georg: 2 articles (05/2004 - 03/2003)
8. Constant, I: 1 article (11/2018)
9. Fain, O: 1 article (11/2018)
10. Feray, S: 1 article (11/2018)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Hereditary Angioedema Type III:
1. Factor XII (Hageman Factor)IBA
2. Angiotensin-Converting Enzyme Inhibitors (ACE Inhibitors)IBA
3. icatibantIBA
4. Angiotensin Receptor AntagonistsIBA
5. Bradykinin Receptors (Bradykinin Receptor)IBA
6. Peptide Hydrolases (Proteases)FDA Link
7. Estrogens (Estrogen)FDA Link
8. Oral ContraceptivesIBA

Therapies and Procedures

1. Hormone Replacement Therapy (Therapy, Hormone Replacement)