A de novo myeloproliferation arising from an abnormal stem cell. It is characterized by the replacement of bone marrow by fibrous tissue, a process that is mediated by CYTOKINES arising from the abnormal clone.
Also Known As:
Myelosclerosis; Agnogenic Myeloid Metaplasia; Bone Marrow Fibrosis; Chronic Idiopathic Myelofibrosis; Fibrosis, Bone Marrow; Idiopathic Myelofibrosis; Myelofibrosis; Myelofibrosis With Myeloid Metaplasia; Myeloid Metaplasia; Myelosis, Nonleukemic; Agnogenic Myeloid Metaplasias; Bone Marrow Fibroses; Fibroses, Bone Marrow; Metaplasia, Agnogenic Myeloid; Metaplasia, Myeloid; Metaplasias, Agnogenic Myeloid; Metaplasias, Myeloid; Myelofibroses; Myelofibroses, Primary; Myelofibrosis, Primary; Myeloid Metaplasia, Agnogenic; Myeloid Metaplasias; Myeloid Metaplasias, Agnogenic; Myeloscleroses; Myeloses, Nonleukemic; Nonleukemic Myeloses; Nonleukemic Myelosis; Primary Myelofibroses