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Primary Myelofibrosis (Myelosclerosis)

A de novo myeloproliferation arising from an abnormal stem cell. It is characterized by the replacement of bone marrow by fibrous tissue, a process that is mediated by CYTOKINES arising from the abnormal clone.
Also Known As:
Myelosclerosis; Agnogenic Myeloid Metaplasia; Bone Marrow Fibrosis; Chronic Idiopathic Myelofibrosis; Fibrosis, Bone Marrow; Idiopathic Myelofibrosis; Myelofibrosis; Myelofibrosis With Myeloid Metaplasia; Myeloid Metaplasia; Myelosis, Nonleukemic; Agnogenic Myeloid Metaplasias; Bone Marrow Fibroses; Fibroses, Bone Marrow; Metaplasia, Agnogenic Myeloid; Metaplasia, Myeloid; Metaplasias, Agnogenic Myeloid; Metaplasias, Myeloid; Myelofibroses; Myelofibroses, Primary; Myelofibrosis, Primary; Myeloid Metaplasia, Agnogenic; Myeloid Metaplasias; Myeloid Metaplasias, Agnogenic; Myeloscleroses; Myeloses, Nonleukemic; Nonleukemic Myeloses; Nonleukemic Myelosis; Primary Myelofibroses
Networked: 3562 relevant articles (282 outcomes, 456 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Splenomegaly
2. Primary Myelofibrosis (Myelosclerosis)
3. Polycythemia Vera
4. Neoplasms (Cancer)
5. Anemia

Experts

1. Verstovsek, Srdan: 174 articles (07/2022 - 05/2006)
2. Tefferi, Ayalew: 123 articles (01/2022 - 01/2002)
3. Mesa, Ruben A: 96 articles (01/2022 - 03/2002)
4. Vannucchi, Alessandro M: 84 articles (07/2022 - 06/2004)
5. Barosi, Giovanni: 59 articles (12/2022 - 12/2002)
6. Hoffman, Ronald: 59 articles (07/2022 - 05/2005)
7. Kröger, Nicolaus: 55 articles (05/2022 - 12/2002)
8. Gupta, Vikas: 54 articles (01/2022 - 03/2010)
9. Harrison, Claire N: 51 articles (07/2022 - 07/2005)
10. Passamonti, Francesco: 49 articles (06/2022 - 09/2004)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Primary Myelofibrosis:
1. ruxolitinibIBA
2. Janus Kinase InhibitorsIBA
3. InterferonsIBA
4. Thalidomide (Thalomid)FDA Link
5. Janus KinasesIBA
6. Lenalidomide (CC 5013)FDA Link
7. fedratinibIBA
8. Prednisone (Sone)FDA LinkGeneric
9. SteroidsIBA
10. Cytarabine (Cytosar-U)FDA LinkGeneric

Therapies and Procedures

1. Therapeutics
2. Stem Cell Transplantation
3. Drug Therapy (Chemotherapy)
4. Bone Marrow Transplantation (Transplantation, Bone Marrow)
5. Transplantation