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Idiopathic Pulmonary Fibrosis

A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.
Also Known As:
Familial Idiopathic Pulmonary Fibrosis; Fibrocystic Pulmonary Dysplasia; Fibrosing Alveolitis, Cryptogenic; Idiopathic Fibrosing Alveolitis, Chronic Form; Idiopathic Pulmonary Fibrosis, Familial; Interstitial Pneumonitis, Usual; Pulmonary Fibrosis, Idiopathic; Usual Interstitial Pneumonia; Cryptogenic Fibrosing Alveolitides; Dysplasia, Fibrocystic Pulmonary; Fibrocystic Pulmonary Dysplasias; Fibrosing Alveolitides, Cryptogenic; Idiopathic Pulmonary Fibroses; Interstitial Pneumonia, Usual; Pneumonitides, Usual Interstitial; Pneumonitis, Usual Interstitial; Pulmonary Dysplasia, Fibrocystic; Pulmonary Fibroses, Idiopathic; Usual Interstitial Pneumonias; Usual Interstitial Pneumonitides; Usual Interstitial Pneumonitis; Cryptogenic Fibrosing Alveolitis
Networked: 4980 relevant articles (213 outcomes, 657 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Interstitial Lung Diseases (Interstitial Lung Disease)
2. Lung Diseases (Lung Disease)
3. Pulmonary Fibrosis (Fibrosing Alveolitis)
4. Disease Progression
5. Inflammation (Inflammations)

Experts

1. Maher, Toby M: 73 articles (01/2022 - 04/2009)
2. Richeldi, Luca: 70 articles (11/2022 - 09/2010)
3. Raghu, Ganesh: 69 articles (11/2022 - 08/2003)
4. Flaherty, Kevin R: 64 articles (02/2022 - 01/2003)
5. Martinez, Fernando J: 63 articles (11/2022 - 01/2003)
6. Crestani, Bruno: 58 articles (01/2022 - 04/2003)
7. Azuma, Arata: 54 articles (01/2022 - 02/2005)
8. Brown, Kevin K: 52 articles (01/2022 - 01/2004)
9. Kaminski, Naftali: 52 articles (01/2022 - 04/2002)
10. Cottin, Vincent: 50 articles (04/2022 - 06/2007)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Idiopathic Pulmonary Fibrosis:
1. pirfenidoneIBA
2. nintedanibIBA
3. Adrenal Cortex Hormones (Corticosteroids)IBA
4. Cyclophosphamide (Cytoxan)FDA LinkGeneric
5. Bleomycin (Blenoxane)FDA LinkGeneric
6. Acetylcysteine (Siran)FDA LinkGeneric
7. CollagenIBA
8. Tyrosine Kinase InhibitorsIBA
9. ThrombomodulinIBA
10. Antifibrotic AgentsIBA

Therapies and Procedures

1. Therapeutics
2. Lung Transplantation
3. Drug Therapy (Chemotherapy)
4. Transplantation
5. Hemoperfusion