|1.||Malignant Atrophic Papulosis
|1.||Magro, Cynthia M: 4 articles (01/2015 - 11/2002)|
|2.||Hanneken, Sandra: 3 articles (01/2014 - 03/2006)|
|3.||Betz, Regina C: 3 articles (01/2014 - 03/2006)|
|4.||Kruse, Roland: 3 articles (01/2014 - 03/2006)|
|5.||Shapiro, Lee: 2 articles (01/2015 - 04/2011)|
|6.||El Shabrawi-Caelen, Laila: 2 articles (01/2014 - 12/2004)|
|7.||Pasternack, Sandra M: 2 articles (01/2014 - 03/2006)|
|8.||Yu, Hong: 2 articles (01/2014 - 06/2013)|
|9.||Scheinfeld, Noah: 2 articles (06/2013 - 01/2011)|
|10.||Shapiro, Lee S: 2 articles (01/2013 - 01/2013)|
01/01/2015 - "Given the efficacy of eculizumab in the treatment of the acute thrombotic phase of Degos disease/MAP, the patient received this drug, resulting in rapid resolution of signs and symptoms associated with her multiorgan failure. "
01/01/2013 - "We recently discovered the use of eculizumab as a salvage drug in the treatment of near fatal Malignant atrophic papulosis (MAP). "
01/01/2013 - "The effects of Eculizumab on the pathology of malignant atrophic papulosis."
11/01/1995 - "Absence of antiphospholipid and anti-endothelial cell antibodies in malignant atrophic papulosis: a study of 15 cases."
01/01/1967 - "[Malignant atrophic papulosis with presence of anti-artery antibodies]."
01/01/2013 - "Immunohistochemical staining involving antibodies to SDF-1/CXCL12 was performed on 3 skin biopsy specimens taken from 2 patients with Degos disease, 1 from a patient with antiphospholipid syndrome, 1 from a patient with cryoglobulinemia, and 2 from healthy control subjects. "
08/01/2015 - "Dowling-Degos disease (DDD) is a rare inherited pigmentary disorder characterised by reticulate pigmentation at flexural sites. "
06/01/2014 - "Reticulate pigmentary disorders include the rare autosomal dominant Galli-Galli disease (GGD) and Dowling-Degos disease (DDD). "
01/01/2014 - "Dowling-Degos disease (DDD) is an autosomal dominant genodermatosis characterized by reticular pigmented anomaly mainly affecting flexures. "
12/01/2013 - "Dowling-Degos disease (DDD) is a rare, benign, autosomal dominant disorder characterized by reticulated pigmentation on flexural areas. "
08/03/2011 - "Reticulate acropigmentation of Kitamura (RAK) and Dowling-Degos Disease (DDD) are rare genodermatosis inherited as an autosomal dominant trait with variable penetrance. "
|6.||Dental Porcelain (Porcelain)IBA
01/01/2007 - "Degos disease is a rare disorder, characterized by the development of typical atrophic porcelain-white macules on the trunk and extremities. "
04/01/2001 - "Many papules demonstrated the classic porcelain-white centers characteristic of Degos' disease, but others exhibited different clinical morphologies that corresponded to the evolutionary stages of papules originally described by Degos. "
01/01/2013 - "DEFINITION OF THE DISEASE: Malignant atrophic papulosis (MAP), described independently by Köhlmeier and Degos et al., is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and surrounding teleangiectatic rim. "
01/01/2010 - "Multiple atrophic, porcelain-white, scar-like papules and plaques with dusky, erythematous borders, suggestive of malignant atrophic papulosis, were noted on the patient's back. "
11/01/2004 - "Degos' disease or atrophic malignant papulosis is defined by porcelain white cutaneous lesions with atrophic scarring, often associated with severe and fatal systemic involvement (visceral and neurological). "
|7.||Keratin-5 (Keratin 5)IBA
01/01/2011 - "Dowling-Degos disease is caused by one of several loss-of-function mutations in the keratin 5 gene. "
02/01/2007 - "A heterozygous frameshift mutation in the V1 domain of keratin 5 in a family with Dowling-Degos disease."
03/01/2006 - "Loss-of-function mutations in the keratin 5 gene lead to Dowling-Degos disease."
07/01/2012 - "Dowling-Degos disease (DDD; MIM 179850) is an autosomal dominant genodermatosis caused by mutations in keratin 5 gene (KRT5). "
07/01/2012 - "A novel heterozygous nonsense mutation of keratin 5 in a Chinese family with Dowling-Degos disease."
|8.||Lupus Coagulation Inhibitor (Lupus Anticoagulant)IBA
10/01/1998 - "We report the case of a 44-year-old woman with Degos' disease who also had a lupus anticoagulant. "
09/08/1984 - "Degos' disease: association with anticardiolipin antibodies and the lupus anticoagulant."
01/01/2006 - "A fatal case of malignant atrophic papulosis (Degos' disease) in a man with factor V Leinden mutation and lupus anticoagulant."
01/01/2014 - "Successful treatment of neurological malignant atrophic papulosis in child by corticosteroid combined with intravenous immunoglobulin."
07/01/2007 - "The use of intravenous immunoglobulin in cutaneous and recurrent perforating intestinal Degos disease (malignant atrophic papulosis)."
01/01/2015 - "This article reviews 9 challenging vasculitis mimickers: fibromuscular dysplasia, calciphylaxis, segmental arterial mediolysis, antiphospholipid syndrome, hypereosinophilic syndrome, lymphomatoid granulomatosis, malignant atrophic papulosis, livedoid vasculopathy, and immunoglobulin G4-related disease. "
|10.||Aspirin (Acetylsalicylic Acid)FDA LinkGeneric
01/01/1992 - "Three years later he was diagnosed as Degos disease by skin biopsy, and treatment with aspirin was started. "
08/01/2001 - "The combination of pentoxifylline and aspirin should be considered when planning treatment strategies for malignant atrophic papulosis."
11/01/1978 - "Malignant atrophic papulosis: treatment with aspirin and dipyridamole."
12/01/2013 - "Treatment of Dowling-Degos disease with fractional Er:YAG laser."
11/01/2003 - "Treatment of Dowling-Degos disease with Er:YAG-laser: results after 2.5 years."
08/01/2002 - "Our case suggest that treatment with the Er:YAG laser might be a successful strategy in Dowling-Degos disease."
08/01/2002 - "A 44-year-old woman suffering from Dowling-Degos disease was treated with the Er:YAG laser pulse energy between 1,000 and 1,200 mJ, three consecutive passes. "
08/01/2002 - "To determine the effectiveness of Er:YAG laser in Dowling-Degos disease. "
01/01/2015 - "Results of endoscopy and laparotomy in our patient with malignant atrophic papulosis were compared to those in the literature. "
01/01/2015 - "PubMed was used for a literature search using the keywords malignant atrophic papulosis, Degos disease, endoscopy, laparoscopy and laparotomy. "
08/01/1999 - "Two months after cutaneous biopsies were taken, the patient developed ptosis and an episode of acute abdominal pain; intestinal perforation and many characteristic lesions of visceral Degos disease involving the entire small bowel were noted at laparotomy."
02/01/1977 - "The etiology of nontraumatic small bowel perforations in 24 operated patients was as follows: strangulation in five, diverticulum in four, foreign bodies in four, idiopathic in three, Crogn's disease in two, malignant atrophic papulosis of Degos (MAP) in two, and tuberculosis, carcinoid tumor, radiotherapy, and iatrogenic in one. "