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Histiocytic Sarcoma

Malignant neoplasms composed of MACROPHAGES or DENDRITIC CELLS. Most histiocytic sarcomas present as localized tumor masses without a leukemic phase. Though the biological behavior of these neoplasms resemble lymphomas, their cell lineage is histiocytic not lymphoid.
Also Known As:
True Histiocytic Lymphoma; True Malignant Histiocytosis; Histiocytic Lymphoma, True; Histiocytic Lymphomas, True; Histiocytic Sarcomas; Histiocytoses, Malignant; Histiocytoses, True Malignant; Histiocytosis, True Malignant; Lymphoma, True Histiocytic; Lymphomas, True Histiocytic; Malignant Histiocytoses; Malignant Histiocytoses, True; Malignant Histiocytosis, True; Sarcoma, Histiocytic; Sarcomas, Histiocytic; True Histiocytic Lymphomas; True Malignant Histiocytoses; Histiocytosis, Malignant; Malignant Histiocytosis
Networked: 427 relevant articles (20 outcomes, 40 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Neoplasms (Cancer)
2. Acute Myeloid Leukemia (Acute Myelogenous Leukemia)
3. Fever (Fevers)
4. Carcinoma (Carcinomatosis)
5. Chromosome Aberrations (Chromosome Abnormalities)

Experts

1. Bonkobara, Makoto: 7 articles (03/2022 - 12/2006)
2. Baumgärtner, Wolfgang: 6 articles (05/2022 - 01/2016)
3. Puff, Christina: 6 articles (05/2022 - 01/2016)
4. Rohn, Karl: 4 articles (05/2022 - 01/2016)
5. Tamura, Kyoichi: 4 articles (03/2022 - 09/2007)
6. Nakayama, Hiroyuki: 4 articles (08/2021 - 12/2003)
7. Uchida, Kazuyuki: 4 articles (08/2021 - 12/2003)
8. Ohno, Koichi: 4 articles (07/2019 - 06/2009)
9. Tsujimoto, Hajime: 4 articles (07/2019 - 06/2009)
10. Hornick, Jason L: 4 articles (01/2019 - 11/2007)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Histiocytic Sarcoma:
1. Doxorubicin (Adriamycin)FDA LinkGeneric
2. NimustineIBA
3. Lomustine (CCNU)FDA Link
4. trametinibIBA
5. Mitogen-Activated Protein Kinase Kinases (MEKs)IBA
6. Dasatinib (BMS 354825)FDA Link
7. Thalidomide (Thalomid)FDA Link
8. Vincristine (Oncovin)FDA LinkGeneric
9. Cyclophosphamide (Cytoxan)FDA LinkGeneric
10. Cytarabine (Cytosar-U)FDA LinkGeneric

Therapies and Procedures

1. Radiotherapy
2. Combination Drug Therapy (Combination Chemotherapy)
3. Bone Marrow Transplantation (Transplantation, Bone Marrow)
4. Stem Cell Transplantation
5. Drug Therapy (Chemotherapy)