A spectrum of disorders characterized by clonal expansions of the peripheral blood LYMPHOCYTE populations known as large granular lymphocytes which contain abundant cytoplasm and azurophilic granules. Subtypes develop from either CD3-negative NATURAL KILLER CELLS or CD3-positive T-CELLS. The clinical course of both subtypes can vary from spontaneous regression to progressive, malignant disease.
Also Known As:
Leukemia, Large Granular Lymphocytic; Aggressive NK Cell Leukemia; Aggressive Natural Killer Cell Leukemia; LGL Leukemia; Large Granular Lymphocyte Leukemia; Large Granular Lymphocytosis; Leukemia, LGL; Leukemia, NK-LGL; Leukemia, T-LGL; Lymphoproliferative Disease of Granular Lymphocytes; Lymphoproliferative Disease of Large Granular Lymphocytes; NK-Cell Large Granular Lymphocytic Leukemia; NK-LGL Leukemia; T-Cell Large Granular Lymphocyte Leukemia; T-LGL Leukemia; Granular Lymphocytoses, Large; Granular Lymphocytosis, Large; LGL Leukemias; Large Granular Lymphocytoses; Leukemia, NK LGL; Leukemia, T Cell Large Granular Lymphocytic; Leukemia, T LGL; Leukemias, LGL; Leukemias, NK-LGL; Leukemias, T-LGL; Lymphocytoses, Large Granular; Lymphocytosis, Large Granular; NK Cell Large Granular Lymphocytic Leukemia; NK LGL Leukemia; NK-LGL Leukemias; T Cell Large Granular Lymphocyte Leukemia; T Cell Large Granular Lymphocytic Leukemia; T LGL Leukemia; T-LGL Leukemias; Leukemia, Lymphocytic, Large Granular; Leukemia, Natural Killer Cell Large Granular Lymphocytic; Leukemia, T-Cell Large Granular Lymphocytic; Natural Killer Cell Large Granular Lymphocytic Leukemia; T-Cell Large Granular Lymphocytic Leukemia