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X-Linked Combined Immunodeficiency Diseases (X Linked Severe Combined Immunodeficiency)

Forms of combined immunodeficiency caused by mutations in the gene for INTERLEUKIN RECEPTOR COMMON GAMMA SUBUNIT. Both severe and non-severe subtypes of the disease have been identified.
Also Known As:
X Linked Severe Combined Immunodeficiency; Combined Immunodeficiency, X-Linked; Immunodeficiency 4; Immunodeficiency 6; Immunodeficiency Diseases, X-Linked Combined; SCID, X-Linked; SCIDX; SCIDX1; Severe Combined Immunodeficiency, X-Linked; Severe Combined Immunodeficiency, X-Linked, T Cell Negative, B Cell Positive, NK Cell Negative; Severe Combined Immunodeficiency, X-Linked, T Cell-Negative, B Cell-Positive, NK Cell-Negative; X-Linked Combined Immunodeficiency; X-Linked Immunodeficiency Disease; X-Linked Immunodeficiency Syndrome; X-Linked SCID; X-SCID; XSCID; Combined Immunodeficiency, X Linked; Immunodeficiency Disease, X-Linked; Immunodeficiency Diseases, X Linked Combined; Immunodeficiency Diseases, X-Linked; Immunodeficiency Syndrome, X-Linked; Immunodeficiency Syndromes, X-Linked; Immunodeficiency, X-Linked Combined; SCID, X Linked; SCIDs, X-Linked; Severe Combined Immunodeficiency, X Linked; X Linked Combined Immunodeficiency; X Linked Combined Immunodeficiency Diseases; X Linked Immunodeficiency Disease; X Linked Immunodeficiency Syndrome; X Linked SCID; X-Linked Combined Immunodeficiencies; X-Linked Immunodeficiency Diseases; X-Linked Immunodeficiency Syndromes; X-Linked SCIDs; X-Linked Severe Combined Immunodeficiency
Networked: 304 relevant articles (14 outcomes, 30 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. X-Linked Combined Immunodeficiency Diseases (X Linked Severe Combined Immunodeficiency)
2. Chronic Granulomatous Disease
3. Severe combined immunodeficiency due to adenosine deaminase deficiency
4. Wiskott-Aldrich Syndrome
5. Leukemia

Experts

1. Leonard, Warren J: 12 articles (01/2019 - 11/2002)
2. Thrasher, Adrian J: 11 articles (06/2018 - 04/2002)
3. Malech, Harry L: 9 articles (10/2020 - 07/2002)
4. De Ravin, Suk See: 6 articles (10/2020 - 07/2007)
5. Gaspar, H Bobby: 6 articles (06/2018 - 12/2004)
6. Fischer, Alain: 6 articles (10/2014 - 04/2002)
7. Hacein-Bey-Abina, Salima: 6 articles (10/2014 - 04/2002)
8. Kumaki, Satoru: 6 articles (09/2013 - 09/2002)
9. Felsburg, Peter J: 6 articles (06/2009 - 01/2002)
10. Kohn, Donald B: 5 articles (01/2021 - 05/2010)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to X-Linked Combined Immunodeficiency Diseases:
1. Adenosine DeaminaseIBA
2. Interleukin-15 (Interleukin 15)IBA
3. Interleukin-2 Receptors (IL 2 Receptor)IBA
4. favipiravirIBA
5. Zanamivir (Relenza)FDA Link
6. adenine deaminaseIBA
7. Interleukin-4 (Interleukin 4)IBA
8. Interleukin-2 (IL2)IBA
9. Complementary DNA (cDNA)IBA
10. Interleukin-13IBA

Therapies and Procedures

1. Transplantation
2. Therapeutics
3. Bone Marrow Transplantation (Transplantation, Bone Marrow)
4. Stem Cell Transplantation
5. Bioreactors (Bioreactor)