Isovaleryl-CoA Dehydrogenase (Isovaleryl-Coenzyme A Dehydrogenase)
A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA).
Also Known As:
Isovaleryl-Coenzyme A Dehydrogenase; Isovaleryl CoA Dehydrogenase; CoA Dehydrogenase, Isovaleryl; Dehydrogenase, Isovaleryl CoA; Dehydrogenase, Isovaleryl-CoA; Dehydrogenase, Isovaleryl-Coenzyme A; Isovaleryl Coenzyme A Dehydrogenase
Networked: 45
relevant articles (1 outcomes,
1 trials/studies)
Relationship Network
Bio-Agent Context: Research Results
Experts
1. | Vockley, Jerry:
3 articles
(09/2021 - 05/2006)
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2. | Ensenauer, Regina:
2 articles
(03/2018 - 05/2006)
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3. | Sakamoto, Osamu:
2 articles
(06/2017 - 12/2011)
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4. | Vockley, J:
2 articles
(03/2000 - 02/2000)
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5. | Alodaib, Ahmad N:
1 article
(09/2021)
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6. | D'Annibale, Olivia M:
1 article
(09/2021)
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7. | Karunanidhi, Anuradha:
1 article
(09/2021)
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8. | Kochersperger, Catherine:
1 article
(09/2021)
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9. | Koppes, Erik A:
1 article
(09/2021)
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10. | Mohsen, Al-Walid:
1 article
(09/2021)
|
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