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Isovaleryl-CoA Dehydrogenase (Isovaleryl-Coenzyme A Dehydrogenase)

A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA).
Also Known As:
Isovaleryl-Coenzyme A Dehydrogenase; Isovaleryl CoA Dehydrogenase; A Dehydrogenase, Isovaleryl-Coenzyme; CoA Dehydrogenase, Isovaleryl; Dehydrogenase, Isovaleryl CoA; Dehydrogenase, Isovaleryl-CoA; Dehydrogenase, Isovaleryl-Coenzyme A; Isovaleryl Coenzyme A Dehydrogenase
Networked: 4 relevant articles (0 outcomes, 1 trials/studies)

Bio-Agent Context: Research Results

Experts

1. Cai, Wei: 1 article (07/2013)
2. Yu, Yong-Guo: 1 article (07/2013)
3. Bei, Fei: 1 article (07/2013)
4. Jia, Jia: 1 article (07/2013)
5. Zheng, Zhao-Jing: 1 article (07/2013)
6. Fu, Qi-Hua: 1 article (07/2013)
7. Sun, Jian-Hua: 1 article (07/2013)
8. Wijnberg, I D: 1 article (05/2008)
9. Wanders, R J A: 1 article (05/2008)
10. Ruiter, J P N: 1 article (05/2008)

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3. Muscular Diseases (Myopathy)
4. Metabolic Diseases (Metabolic Disease)

Related Drugs and Biologics

1. Semaphorin-3A
2. 4-Butyrolactone (gamma Butyrolactone)
3. fascin
4. Acyl-CoA Dehydrogenase (Medium-Chain Acyl-Coenzyme A Dehydrogenase)
5. Butyryl-CoA Dehydrogenase (Short-Chain Acyl-CoA Dehydrogenase)
6. Oxidoreductases
7. isovaleric Acidemia