HOMEPRODUCTSCOMPANYCONTACTFAQResearchDictionaryPharmaSign Up FREE or Login

Succinate-Semialdehyde Dehydrogenase (Succinic Semialdehyde Dehydrogenase)

An enzyme that plays a role in the GLUTAMATE and butanoate metabolism pathways by catalyzing the oxidation of succinate semialdehyde to SUCCINATE using NAD+ as a coenzyme. Deficiency of this enzyme, causes 4-hydroxybutyricaciduria, a rare inborn error in the metabolism of the neurotransmitter 4-aminobutyric acid (GABA).
Also Known As:
Succinic Semialdehyde Dehydrogenase; NAD(+)-Dependent Succinic Semialdehyde Dehydrogenase; Succinate Semialdehyde Dehydrogenase; Dehydrogenase, Succinate Semialdehyde; Dehydrogenase, Succinate-Semialdehyde; Dehydrogenase, Succinic Semialdehyde; Semialdehyde Dehydrogenase, Succinate; Semialdehyde Dehydrogenase, Succinic
Networked: 112 relevant articles (2 outcomes, 5 trials/studies)

Relationship Network

Bio-Agent Context: Research Results

Experts

1. Gibson, K Michael: 33 articles (11/2020 - 07/2002)
2. Pearl, Phillip L: 19 articles (11/2021 - 01/2003)
3. Gibson, K M: 16 articles (04/2017 - 10/2001)
4. Jakobs, Cornelis: 13 articles (09/2015 - 07/2002)
5. Snead, O Carter: 13 articles (03/2009 - 07/2002)
6. Jakobs, C: 10 articles (08/2009 - 10/2001)
7. Pearl, P L: 6 articles (08/2009 - 05/2003)
8. Gupta, Maneesh: 6 articles (04/2006 - 07/2002)
9. Roullet, Jean-Baptiste: 5 articles (11/2020 - 01/2018)
10. Salomons, Gajja S: 5 articles (11/2020 - 12/2003)

Related Diseases

1. succinic semialdehyde dehydrogenase deficiency
2. Status Epilepticus (Complex Partial Status Epilepticus)
3. Ischemia
4. Seizures (Absence Seizure)
5. Ataxia (Dyssynergia)

Related Drugs and Biologics

1. gamma-Aminobutyric Acid (GABA)
2. 4-hydroxybutyric acid
3. Vigabatrin
4. Taurine
5. Enzymes
6. Glutamate Decarboxylase (Decarboxylase, Glutamate)
7. Neuroprotective Agents
8. Antioxidants
9. ebselen
10. Aminobutyrates (Aminobutyric Acid)

Related Therapies and Procedures

1. Transcranial Magnetic Stimulation