An enzyme that catalyzes the HYDROXYLATION of gamma-butyrobetaine to L-CARNITINE. It is the last enzyme in the biosynthetic pathway of L-CARNITINE and is dependent on alpha-ketoglutarate; IRON; ASCORBIC ACID; and OXYGEN.
Also Known As:
4-Trimethylaminobutyrate, 2-Oxoglutarate Oxygen Oxidoreductase (3-Hydroxylating); Butyrobetaine Hydroxylase; Trimethylaminobutyrate Hydroxylase; gamma-Butyrobetaine Hydroxylase; gamma-Butyrobetaine, 2-Oxoglutarate Dioxygenase; gamma-Butyrobetaine,2-Oxoglutarate Dioxygenase; 2-Oxoglutarate Dioxygenase gamma-Butyrobetaine; Dioxygenase gamma-Butyrobetaine, 2-Oxoglutarate; Dioxygenase, gamma-Butyrobetaine; Dioxygenase, gamma-Butyrobetaine,2-Oxoglutarate; Hydroxylase, Butyrobetaine; Hydroxylase, Trimethylaminobutyrate; Hydroxylase, gamma-Butyrobetaine; gamma Butyrobetaine Dioxygenase; gamma Butyrobetaine Hydroxylase; gamma Butyrobetaine, 2 Oxoglutarate Dioxygenase; gamma Butyrobetaine,2 Oxoglutarate Dioxygenase