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Distal Myopathies (Distal Muscular Dystrophy)

A heterogeneous group of genetic disorders characterized by progressive MUSCULAR ATROPHY and MUSCLE WEAKNESS beginning in the hands, the legs, or the feet. Most are adult-onset autosomal dominant forms. Others are autosomal recessive.
Also Known As:
Distal Muscular Dystrophy; Distal Myopathy; Welander Distal Myopathy; Distal Muscular Dystrophies; Distal Myopathy 1; Distal Myopathy Markesbery-Griggs Type; Finnish-Markesbery Muscular Dystrophy; Laing Distal Myopathy; Laing Early-Onset Distal Myopathy; Muscular Dystrophy, Distal, Late-Onset, Autosomal Dominant; Myopathy, Distal 1; Myopathy, Distal, Early-Onset, Autosomal Dominant; Myopathy, Distal, Swedish; Myopathy, Late Distal Hereditary; Tardive Tibial Muscular Dystrophy; Tibial Muscular Dystrophy; Tibial Muscular Dystrophy, Tardive; Udd Distal Myopathy; Udd Myopathy; Udd-Markesbery Muscular Dystrophy; Distal 1 Myopathies; Distal 1 Myopathy; Distal Myopathy 1s; Distal Myopathy Markesbery Griggs Type; Distal Myopathy, Laing; Distal Myopathy, Udd; Distal Myopathy, Welander; Finnish Markesbery Muscular Dystrophy; Laing Early Onset Distal Myopathy; Muscular Dystrophies, Distal; Muscular Dystrophies, Tibial; Muscular Dystrophy, Finnish-Markesbery; Muscular Dystrophy, Tibial; Muscular Dystrophy, Udd-Markesbery; Myopathies, Distal; Myopathies, Distal 1; Myopathy 1, Distal; Myopathy 1s, Distal; Myopathy, Distal; Myopathy, Laing Distal; Myopathy, Udd; Myopathy, Udd Distal; Udd Markesbery Muscular Dystrophy; Muscular Dystrophy, Distal
Networked: 216 relevant articles (1 outcomes, 7 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Congenital Structural Myopathies (Centronuclear Myopathy)
2. Distal Myopathies (Distal Muscular Dystrophy)
3. Myofibrillar Myopathy
4. Muscular Dystrophies (Muscular Dystrophy)
5. Amyotrophic Lateral Sclerosis (Lou Gehrig's Disease)

Experts

1. Udd, Bjarne: 27 articles (08/2022 - 09/2002)
2. Hackman, Peter: 16 articles (08/2022 - 09/2002)
3. Vihola, Anna: 14 articles (08/2022 - 09/2002)
4. Nishino, Ichizo: 12 articles (01/2019 - 12/2004)
5. Sarparanta, Jaakko: 10 articles (08/2022 - 09/2002)
6. Lochmüller, Hanns: 8 articles (01/2018 - 12/2003)
7. Udd, B: 8 articles (10/2016 - 04/2001)
8. Richard, Isabelle: 7 articles (07/2015 - 09/2002)
9. Hayashi, Yukiko K: 7 articles (01/2015 - 10/2004)
10. Jonson, Per Harald: 6 articles (08/2022 - 04/2013)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Distal Myopathies:
1. Pyridostigmine Bromide (Pyridostigmine)FDA LinkGeneric
2. ConnectinIBA
3. DesminIBA
4. AnoctaminsIBA
5. DNA (Deoxyribonucleic Acid)IBA
6. LectinsIBA
7. AgglutininsIBA
8. Myosin SubfragmentsIBA
9. DysferlinIBA
10. Proteins (Proteins, Gene)FDA Link

Therapies and Procedures

1. Therapeutics
2. Kidney Transplantation
3. Heart Transplantation (Grafting, Heart)
4. Nephrectomy
5. Critical Care (Surgical Intensive Care)