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Sphingolipid Activator Proteins

A family of glycoprotein cofactors that are required for the efficient catabolization of SPHINGOLIPIDS by specific acid hydrolases such as GLUCOSYLCERAMIDASE; GALACTOCEREBROSIDASE; BETA-N-ACETYLHEXOSAMINIDASE; and CEREBROSIDE-SULFATASE.
Also Known As:
Cerebroside Sulfate Activator Protein; G(M1) Ganglioside Activating Factor; GM1 Activator Protein; Ganglioside Degradation Activator Protein; Ganglioside Hydrolysis Activator Proteins; Hexosaminidase A Activating Protein; Hexosaminidase Activating Factor; G(M1) Activator Protein
Networked: 15 relevant articles (0 outcomes, 2 trials/studies)

Bio-Agent Context: Research Results

Experts

1. Sandhoff, Konrad: 1 article (11/2016)
2. Asfaw, Befekadu: 1 article (02/2009)
3. Berná, Linda: 1 article (02/2009)
4. Chrastina, Petr: 1 article (02/2009)
5. Dvoráková, Lenka: 1 article (02/2009)
6. Elleder, Milan: 1 article (02/2009)
7. Harzer, Klaus: 1 article (02/2009)
8. Hrebícek, Martin: 1 article (02/2009)
9. Krägeloh-Mann, Ingeborg: 1 article (02/2009)
10. Kuchar, Ladislav: 1 article (02/2009)

Related Diseases

1. Neuronal Ceroid-Lipofuscinoses (Neuronal Ceroid Lipofuscinosis)
2. Sphingolipidoses (Sphingolipidosis)
3. Lysosomal Storage Diseases (Lysosomal Storage Disease)
4. Neurodegenerative Diseases (Neurodegenerative Disease)
5. Mucolipidoses (Sialidosis)

Related Drugs and Biologics

1. Saposins
2. Hydrolases
3. Glycosphingolipids
4. Lipids
5. Mitochondrial Proton-Translocating ATPases (Mitochondrial ATP Synthase)
6. Sulfoglycosphingolipids (Sulfatides)
7. Sphingolipids
8. Proteins (Proteins, Gene)
9. Phosphotransferases (Kinase)
10. Membrane Lipids