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Cutaneous Mastocytosis

Skin lesions due to abnormal infiltration of MAST CELLS. Cutaneous mastocytosis is confined to the skin without the involvement of other tissues or organs, and is mostly found in children. The three major variants are: URTICARIA PIGMENTOSA; diffuse cutaneous mastocytosis; and SOLITARY MASTOCYTOMA OF SKIN.
Also Known As:
Mastocytosis, Cutaneous; Bullous Mastocytoses; Bullous Mastocytosis; Cutaneous Mastocytoses; Cutaneous Mastocytoses, Diffuse; Cutaneous Mastocytosis, Diffuse; Mastocytoses, Bullous; Mastocytoses, Cutaneous; Mastocytoses, Skin; Mastocytosis, Skin; Skin Mastocytoses; Mastocytosis, Bullous; Mastocytosis, Diffuse Cutaneous; Skin Mastocytosis
Networked: 140 relevant articles (6 outcomes, 10 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Mastocytosis
2. Mast Cell Activation Syndrome
3. Mast Cell Activation Disorders (Mast-Cell Disease)
4. Hypereosinophilic Syndrome (Loeffler Endocarditis)
5. Systemic Mastocytosis

Experts

1. Lange, Magdalena: 4 articles (12/2021 - 01/2018)
2. Hermine, Olivier: 4 articles (01/2021 - 12/2010)
3. Nedoszytko, Bogusław: 3 articles (12/2021 - 05/2014)
4. Niedoszytko, Marek: 3 articles (12/2021 - 10/2018)
5. Dubreuil, Patrice: 3 articles (01/2021 - 12/2010)
6. Brockow, K: 3 articles (07/2015 - 02/2008)
7. Metcalfe, Dean D: 2 articles (01/2022 - 01/2021)
8. Nowicki, Roman J: 2 articles (12/2021 - 05/2014)
9. Ługowska-Umer, Hanna: 2 articles (12/2021 - 10/2018)
10. Orfao, Alberto: 2 articles (10/2021 - 06/2010)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Cutaneous Mastocytosis:
1. Omalizumab (Xolair)FDA Link
2. Tryptases (Tryptase)IBA
3. Imatinib Mesylate (Gleevec)FDA Link
4. Immunoglobulin E (IgE)IBA
5. Interferon-alpha (Interferon Alfa)IBA
6. Hydroxychloroquine (Plaquenil)FDA LinkGeneric
7. Fluticasone (Cutivate)FDA LinkGeneric
8. Ficusin (Psoralen)IBA
9. Epinephrine (Adrenaline)FDA LinkGeneric
10. AntibodiesIBA

Therapies and Procedures

1. Therapeutics
2. Photochemotherapy (Photodynamic Therapy)
3. Phototherapy (Light Therapy)
4. Radiotherapy
5. Drug Therapy (Chemotherapy)