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Erdheim-Chester Disease

A rare form of non-Langerhans-cell histiocytosis (HISTIOCYTOSIS, NON-LANGERHANS-CELL) with onset in middle age. The systemic disease is characterized by infiltration of lipid-laden macrophages, multinucleated giant cells, an inflammatory infiltrate of lymphocytes and histiocytes in the bone marrow, and a generalized sclerosis of the long bones.
Also Known As:
Erdheim Chester Disease; Lipid Granulomatosis; Granulomatosis, Lipid
Networked: 93 relevant articles (10 outcomes, 2 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Juvenile Xanthogranuloma
2. Fatigue
3. Neoplasms (Cancer)
4. Langerhans-Cell Histiocytosis (Histiocytosis, Langerhans Cell)
5. Non-Langerhans-Cell Histiocytosis (Histiocytosis, Non Langerhans Cell)

Experts

1. Rehák, Z: 5 articles (11/2012 - 01/2011)
2. Mayer, J: 5 articles (11/2012 - 01/2011)
3. Zahradová, L: 5 articles (11/2012 - 01/2011)
4. Szturz, P: 5 articles (11/2012 - 01/2011)
5. Adam, Z: 5 articles (11/2012 - 01/2011)
6. Koukalová, R: 5 articles (11/2012 - 01/2011)
7. Pour, L: 5 articles (11/2012 - 01/2011)
8. Kurzrock, Razelle: 4 articles (07/2014 - 11/2005)
9. Hájek, R: 4 articles (11/2012 - 01/2011)
10. Král, Z: 4 articles (11/2012 - 01/2011)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Erdheim-Chester Disease:
1. Interferon-alpha (Interferon Alfa)FDA Link
2. Interleukin 1 Receptor Antagonist Protein (Anakinra)FDA Link
3. InterferonsIBA
4. CladribineFDA LinkGeneric
5. Interleukin-1 (Interleukin 1)IBA
6. Prednisolone (Predate)FDA LinkGeneric
7. Cyclophosphamide (Cytoxan)FDA LinkGeneric
8. lenalidomide (CC 5013)FDA Link
9. Sirolimus (Rapamycin)FDA Link
10. Prednisone (Sone)FDA LinkGeneric

Therapies and Procedures

1. Aftercare (After-Treatment)
2. Radiotherapy
3. Palliative Care (Palliative Medicine)
4. Drug Therapy (Chemotherapy)
5. Renal Dialysis (Hemodialysis)