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Supravalvular Aortic Stenosis (Aortic Supravalvular Stenosis)

A pathological constriction occurring in the region above the AORTIC VALVE. It is characterized by restricted outflow from the LEFT VENTRICLE into the AORTA.
Also Known As:
Aortic Supravalvular Stenosis; Aortic Stenosis, Supravalvular; Stenosis, Aortic Supravalvular; Stenosis, Supravalvular Aortic; Supravalvar Aortic Stenosis; Supravalvular Stenosis, Aortic; Aortic Supravalvular Stenoses; Stenoses, Aortic Supravalvular; Supravalvular Stenoses, Aortic
Networked: 170 relevant articles (0 outcomes, 11 trials/studies)

Disease Context: Research Results

Related Diseases

1. Aortic Valve Stenosis (Aortic Stenosis)
2. Williams Syndrome (Williams-Beuren Syndrome)
3. Pathologic Constriction (Stenosis)
4. Vascular Diseases (Vascular Disease)
5. Cutis Laxa

Experts

1. Mecham, Robert P: 11 articles (01/2020 - 05/2003)
2. Knutsen, Russell H: 9 articles (01/2020 - 11/2003)
3. Kozel, Beth A: 7 articles (06/2022 - 05/2003)
4. Wagenseil, Jessica E: 6 articles (01/2022 - 09/2005)
5. Faury, Gilles: 5 articles (01/2012 - 11/2003)
6. Li, Dean Y: 5 articles (02/2008 - 11/2003)
7. Urban, Zsolt: 4 articles (03/2016 - 11/2005)
8. Mota, Gustavo Augusto Ferreira: 3 articles (01/2022 - 07/2020)
9. Sant'Ana, Paula Grippa: 3 articles (01/2022 - 07/2020)
10. Vileigas, Danielle Fernandes: 3 articles (01/2022 - 07/2020)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Supravalvular Aortic Stenosis:
1. ElastinIBA
2. LDL Receptors (LDL Receptor)IBA
3. ReninIBA
4. Phosphates (Orthophosphate)IBA
5. Proteins (Proteins, Gene)FDA Link
6. Vitamin DFDA LinkGeneric
7. Fibrillin-1IBA
8. FibrillinsIBA
9. CholesterolIBA
10. DiamondIBA

Therapies and Procedures

1. Transjugular Intrahepatic Portasystemic Shunt
2. Plasmapheresis
3. Arterial Switch Operation
4. Operative Surgical Procedures
5. Coronary Artery Bypass (Coronary Artery Bypass Surgery)