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Myotonic Disorders (Paramyotonia Congenita)

Diseases characterized by MYOTONIA, which may be inherited or acquired. Myotonia may be restricted to certain muscles (e.g., intrinsic hand muscles) or occur as a generalized condition.
Also Known As:
Paramyotonia Congenita; Eulenburg Disease; Eulenburg's Disease; Paralysis Periodica Paramyotonia; Paramyotonia Congenita Without Cold Paralysis; Paramyotonia Congenita of von Eulenberg; Von Eulenberg's Disease; Disorder, Myotonic; Disorders, Myotonic; Myopathy, Myotonic; Myotonic Disorder; Myotonic Myopathies; Myotonic Myopathy; Von Eulenberg Disease; Myopathies, Myotonic; Myotonia Fluctuans
Networked: 190 relevant articles (10 outcomes, 12 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Paralysis (Palsy)
2. Potassium aggravated myotonia
3. Motor Neuron Disease (Primary Lateral Sclerosis)
4. Tetany (Spasmophilia)
5. Spasm (Spasms)

Experts

1. Fontaine, Bertrand: 4 articles (11/2021 - 02/2004)
2. Sternberg, Damien: 4 articles (01/2019 - 02/2004)
3. Sternberg, D: 4 articles (11/2014 - 01/2003)
4. Dengler, R: 4 articles (06/2001 - 01/2000)
5. Jurkat-Rott, Karin: 3 articles (11/2015 - 08/2006)
6. Hanna, Michael G: 3 articles (11/2014 - 01/2011)
7. Takahashi, Masanori P: 3 articles (06/2012 - 11/2007)
8. Meola, G: 3 articles (10/2005 - 01/2000)
9. Schneider, C: 3 articles (01/2002 - 08/2001)
10. Bufler, J: 3 articles (06/2001 - 07/2000)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Myotonic Disorders:
1. Mexiletine (Mexitil)FDA LinkGeneric
2. Sodium Channels (Sodium Channel)IBA
3. Tocainide (Tonocard)FDA Link
4. Acetazolamide (Diamox)FDA LinkGeneric
5. Anti-Arrhythmia AgentsIBA
6. Pyridostigmine Bromide (Pyridostigmine)FDA LinkGeneric
7. Lidocaine (Xylocaine)FDA LinkGeneric
8. Propafenone (Rythmol)FDA LinkGeneric
9. Buprenorphine (Subutex)FDA LinkGeneric
10. PotassiumIBA

Therapies and Procedures

1. Therapeutics
2. Anesthesia
3. Cesarean Section (Caesarean Section)
4. Gastrectomy
5. Electrodes (Electrode)