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Striatonigral Degeneration

A sporadic neurodegenerative disease with onset in middle-age characterized clinically by Parkinsonian features (e.g., MUSCLE RIGIDITY; HYPOKINESIA; stooped posture) and HYPOTENSION. This condition is considered a clinical variant of MULTIPLE SYSTEM ATROPHY. Pathologic features include a prominent loss of neurons in the zona compacta of the SUBSTANTIA NIGRA and PUTAMEN. (From Adams et al., Principles of Neurology, 6th ed, p1075-6)
Also Known As:
Striatonigral Atrophy; Atrophies, Striatonigral; Atrophy, Striatonigral; Degeneration, Striatonigral; Striatonigral Atrophies; Striatonigral Degenerations
Networked: 94 relevant articles (3 outcomes, 16 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Parkinson Disease (Parkinson's Disease)
2. Multiple System Atrophy
3. Parkinsonian Disorders (Parkinsonism)
4. Olivopontocerebellar Atrophies (Olivopontocerebellar Atrophy)
5. Progressive Supranuclear Palsy (Steele Richardson Olszewski Syndrome)

Experts

1. Tison, F: 12 articles (10/2005 - 01/2000)
2. Wenning, G K: 11 articles (08/2005 - 01/2000)
3. Poewe, W: 8 articles (08/2005 - 01/2000)
4. Scherfler, C: 8 articles (08/2005 - 01/2000)
5. Stefanova, Nadia: 7 articles (01/2019 - 08/2003)
6. Ghorayeb, I: 7 articles (10/2005 - 01/2000)
7. Puschban, Z: 7 articles (08/2005 - 01/2000)
8. Poewe, Werner: 6 articles (10/2015 - 08/2003)
9. Wenning, Gregor K: 6 articles (10/2015 - 08/2003)
10. Fernagut, P O: 6 articles (10/2005 - 05/2000)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Striatonigral Degeneration:
1. Levodopa (L Dopa)FDA LinkGeneric
2. Dopamine (Intropin)FDA LinkGeneric
3. Homovanillic AcidIBA
4. CalcineurinIBA
5. Quinolinic AcidIBA
6. SilverIBA
7. Oxidopamine (6 Hydroxydopamine)IBA
8. Neuroprotective AgentsIBA
9. Substance PIBA
10. Glucose (Dextrose)FDA LinkGeneric

Therapies and Procedures

1. Therapeutics
2. Transplantation
3. Pallidotomy
4. Deep Brain Stimulation