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Hyperkalemic Periodic Paralysis

An autosomal dominant familial disorder which presents in infancy or childhood and is characterized by episodes of weakness associated with hyperkalemia. During attacks, muscles of the lower extremities are initially affected, followed by the lower trunk and arms. Episodes last from 15-60 minutes and typically occur after a period of rest following exercise. A defect in skeletal muscle sodium channels has been identified as the cause of this condition. Normokalemic periodic paralysis is a closely related disorder marked by a lack of alterations in potassium levels during attacks of weakness. (Adams et al., Principles of Neurology, 6th ed, p1481)
Also Known As:
Paralysis, Hyperkalemic Periodic; Adynamia Episodica Hereditaria; Adynamia Episodica Hereditaria with or without Myotonia; Familial Hyperkalemic Periodic Paralysis; Gamstorp Disease; Gamstorp Episodic Adynamy; HyperKPP; HyperPP; Hyperkalemic Periodic Paralysis Type 2; Hyperkalemic Periodic Paralysis, Familial; Hyperkaliemic Periodic Paralysis Type 2; Primary Hyperkalemic Periodic Paralysis; Sodium Channel Muscle Disease; Disease, Gamstorp; Myotonic Periodic Paralysis; Paralysis, Periodic, Hyperkalemic, Familial
Networked: 170 relevant articles (4 outcomes, 14 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Hyperkalemic Periodic Paralysis
2. Myotonic Disorders (Paramyotonia Congenita)
3. Myotonia
4. Hypokalemic Periodic Paralysis (Periodic Paralysis, Hypokalemic)
5. Myotonia Congenita (Thomsen Disease)

Experts

1. Hanna, Michael G: 5 articles (07/2021 - 08/2002)
2. Hayward, Lawrence J: 5 articles (01/2020 - 12/2012)
3. Renaud, Jean-Marc: 5 articles (01/2020 - 12/2012)
4. Matthews, Emma: 4 articles (07/2021 - 04/2013)
5. Ammar, Tarek: 4 articles (01/2020 - 06/2014)
6. Lehmann-Horn, F: 3 articles (10/2011 - 01/2000)
7. Fontaine, B: 3 articles (10/2005 - 12/2002)
8. Tan, S Veronica: 2 articles (07/2021 - 01/2020)
9. Männikkö, Roope: 2 articles (01/2020 - 01/2018)
10. Kokunai, Yosuke: 2 articles (11/2018 - 06/2012)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Hyperkalemic Periodic Paralysis:
1. SodiumIBA
2. Phenytoin (Dilantin)FDA LinkGeneric
3. Sodium Chloride Symporter Inhibitors (Diuretics, Thiazide)IBA
4. Triglycerides (Triacylglycerol)IBA
5. Albuterol (Salbutamol)FDA LinkGeneric
6. Hydrochlorothiazide (Esidrix)FDA LinkGeneric
7. Adrenergic Agonists (Adrenergic Receptor Agonist)IBA
8. Acetazolamide (Diamox)FDA LinkGeneric
9. PotassiumIBA
10. Sodium Channels (Sodium Channel)IBA

Therapies and Procedures

1. Therapeutics
2. Electrodes (Electrode)
3. Anesthesia
4. General Anesthesia
5. Intravenous Administration