A slowly progressive autoimmune demyelinating disease of peripheral nerves and nerve roots. Clinical manifestations include weakness and sensory loss in the extremities and enlargement of peripheral nerves. The course may be relapsing-remitting or demonstrate a step-wise progression. Protein is usually elevated in the spinal fluid and cranial nerves are typically spared. GUILLAIN-BARRE SYNDROME features a relatively rapid progression of disease which distinguishes it from this condition. (Adams et al., Principles of Neurology, 6th ed, p1337)
Also Known As:
CIDP; Polyradiculoneuropathy, Chronic Inflammatory; Polyradiculoneuropathy, Chronic Inflammatory Demyelinating; Chronic Inflammatory Polyradiculoneuropathy; Inflammatory Polyradiculopathy, Chronic; Polyneuropathy, Inflammatory Demyelinating, Chronic; Chronic Inflammatory Polyradiculoneuropathies; Chronic Inflammatory Polyradiculopathies; Chronic Inflammatory Polyradiculopathy; Inflammatory Polyradiculoneuropathies, Chronic; Inflammatory Polyradiculoneuropathy, Chronic; Inflammatory Polyradiculopathies, Chronic; Polyradiculoneuropathies, Chronic Inflammatory; Polyradiculopathies, Chronic Inflammatory; Polyradiculopathy, Chronic Inflammatory