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Nervous System Heredodegenerative Disorders

Inherited disorders characterized by progressive atrophy and dysfunction of anatomically or physiologically related neurologic systems.
Also Known As:
Heredodegenerative Disorders, Nervous System; Degenerative Hereditary Diseases, Nervous System; Hereditary Neurodegenerative Diseases; Hereditary-Degenerative Disorders, Nervous System; Nervous System Degenerative Hereditary Diseases; Nervous System Hereditary Degenerative Diseases; Disease, Hereditary Neurodegenerative; Disease, Neurodegenerative Hereditary; Diseases, Hereditary Neurodegenerative; Diseases, Neurodegenerative Hereditary; Hereditary Degenerative Disorders, Nervous System; Hereditary Disease, Neurodegenerative; Hereditary Neurodegenerative Disease; Neurodegenerative Disease, Hereditary; Neurodegenerative Hereditary Disease; Neurodegenerative Hereditary Diseases; Degenerative Disease, Nervous System, Hereditary; Degenerative Hereditary Disorders, Nervous System; Hereditary Diseases, Neurodegenerative; Nervous System Diseases, Degenerative, Hereditary; Neurodegenerative Diseases, Hereditary
Networked: 63 relevant articles (0 outcomes, 5 trials/studies)

Disease Context: Research Results

Related Diseases

1. Dystonic Disorders (Writer's Cramp)
2. Essential Tremor (Essential Tremors)
3. Parkinson Disease (Parkinson's Disease)
4. Hepatolenticular Degeneration (Wilson's Disease)
5. Blindness (Hysterical Blindness)

Experts

1. Sobue, Gen: 5 articles (01/2022 - 11/2006)
2. Katsuno, Masahisa: 4 articles (07/2022 - 11/2006)
3. Ghetti, Bernardino: 4 articles (11/2020 - 08/2004)
4. Vidal, Ruben: 4 articles (11/2020 - 08/2004)
5. Czeredys, Magdalena: 3 articles (01/2018 - 01/2013)
6. Kuznicki, Jacek: 3 articles (01/2018 - 01/2013)
7. Garringer, Holly J: 2 articles (11/2020 - 01/2016)
8. Muhoberac, Barry B: 2 articles (11/2020 - 01/2016)
9. Mikoshiba, Katsuhiko: 2 articles (01/2018 - 08/2012)
10. Methner, Axel: 2 articles (02/2017 - 01/2013)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Nervous System Heredodegenerative Disorders:
1. polyglutamineIBA
2. Proteins (Proteins, Gene)FDA Link
3. DNA (Deoxyribonucleic Acid)IBA
4. Retinaldehyde (Retinal)IBA
5. MetalsIBA
6. FrataxinIBA
7. Androgen Receptors (Androgen Receptor)IBA
8. Mitochondrial Proteins (Mitochondrial Protein)IBA
9. IronIBA
10. Huntingtin ProteinIBA

Therapies and Procedures

1. Therapeutics
2. Chelation Therapy (Therapy, Chelation)