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Acquired Hyperostosis Syndrome (SAPHO Syndrome)

Syndrome consisting of SYNOVITIS; ACNE CONGLOBATA; PALMOPLANTAR PUSTULOSIS; HYPEROSTOSIS; and OSTEITIS. The most common site of the disease is the upper anterior chest wall, characterized by predominantly osteosclerotic lesions, hyperostosis, and arthritis of the adjacent joints. The association of sterile inflammatory bone lesions and neutrophilic skin eruptions is indicative of this syndrome.
Also Known As:
SAPHO Syndrome; Synovitis, Acne, Pustlosis, Hyperostosis, and Osteomyelitis; Acquired Hyperostosis Syndromes; Hyperostosis Syndrome, Acquired; Hyperostosis Syndromes, Acquired; SAPHO Syndromes; Syndrome, Acquired Hyperostosis; Syndrome, SAPHO; Syndromes, Acquired Hyperostosis; Syndromes, SAPHO
Networked: 211 relevant articles (35 outcomes, 16 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Osteitis
2. Acne Vulgaris
3. Synovitis
4. Hyperostosis
5. Osteomyelitis

Experts

1. Li, Chen: 27 articles (01/2022 - 01/2017)
2. Zhang, Wen: 14 articles (01/2022 - 01/2017)
3. Cao, Yihan: 13 articles (01/2022 - 05/2018)
4. Li, Li: 7 articles (06/2022 - 05/2018)
5. Wang, Lun: 7 articles (04/2021 - 07/2019)
6. Wu, Nan: 7 articles (04/2021 - 05/2018)
7. Jing, Hongli: 6 articles (04/2021 - 05/2018)
8. Brzosko, Marek: 5 articles (01/2021 - 01/2013)
9. Przepiera-Będzak, Hanna: 5 articles (01/2021 - 01/2013)
10. Wu, Xia: 5 articles (01/2021 - 05/2018)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Acquired Hyperostosis Syndrome:
1. Pamidronate (Aredia)FDA LinkGeneric
2. Tumor Necrosis Factor-alpha (Tumor Necrosis Factor)IBA
3. Anti-Bacterial Agents (Antibiotics)IBA
4. Adalimumab (Humira)FDA Link
5. Etanercept (Enbrel)FDA Link
6. tofacitinibIBA
7. Interleukin 1 Receptor Antagonist Protein (Anakinra)FDA Link
8. Janus Kinase InhibitorsIBA
9. Diphosphonates (Bisphosphonates)IBA
10. Infliximab (Remicade)FDA Link

Therapies and Procedures

1. Therapeutics
2. Tonsillectomy
3. Biological Therapy
4. Off-Label Use
5. Immunotherapy