An arylsulfatase that catalyzes the hydrolysis of the 4-sulfate groups of the N-acetyl-D-galactosamine 4-sulfate units of chondroitin sulfate and dermatan sulfate. A deficiency of this enzyme is responsible for the inherited lysosomal disease, Maroteaux-Lamy syndrome (MUCOPOLYSACCHARIDOSIS VI). EC 3.1.6.12.
Also Known As:
Arylsulfatase B; Arylsulfatase B1; Arylsulfatase B2; N-Acetylgalactosamine 4-Sulfatase; N-Acetylgalactosamine-4-sulfate Sulfatase; N-Acetylgalactosamine-4-sulphate Sulphatase; 4-Sulfatase, N-Acetylgalactosamine; B1, Arylsulfatase; B2, Arylsulfatase; N Acetylgalactosamine 4 Sulfatase; N Acetylgalactosamine 4 sulfate Sulfatase; N Acetylgalactosamine 4 sulphate Sulphatase; Sulfatase, N-Acetylgalactosamine-4-sulfate; Sulphatase, N-Acetylgalactosamine-4-sulphate; N-Acetyl-D-Galactosamine-4-sulfate 4-sulfohydrolase