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alpha 1-Antitrypsin Deficiency (alpha 1 Antitrypsin Deficiency)

Deficiency of the protease inhibitor ALPHA 1-ANTITRYPSIN that manifests primarily as PULMONARY EMPHYSEMA and LIVER CIRRHOSIS.
Also Known As:
alpha 1 Antitrypsin Deficiency; Deficiencies, alpha 1-Antitrypsin; Deficiency, alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiencies
Networked: 274 relevant articles (6 outcomes, 18 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Liver Diseases (Liver Disease)
2. Panniculitis
3. Hepatolenticular Degeneration (Wilson's Disease)
4. Hepatitis B
5. Emphysema

Experts

1. Stockley, Robert A: 3 articles (08/2009 - 06/2006)
2. Stoller, James K: 3 articles (05/2006 - 12/2002)
3. Bouchecareilh, Marion: 2 articles (08/2021 - 02/2021)
4. Greulich, Timm: 2 articles (01/2021 - 11/2011)
5. Welte, Tobias: 2 articles (01/2021 - 01/2017)
6. Kueppers, Friedrich: 2 articles (12/2020 - 01/2019)
7. Krowka, Michael J: 2 articles (08/2013 - 02/2011)
8. Wencker, Marion: 2 articles (08/2009 - 10/2005)
9. Lawless, Matthew W: 2 articles (01/2008 - 07/2007)
10. Mankan, Arun K: 2 articles (01/2008 - 07/2007)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to alpha 1-Antitrypsin Deficiency:
1. alpha 1-Antitrypsin (alpha 1 Antitrypsin)IBA
2. Protease Inhibitors (Protease Inhibitor)IBA
3. Leukocyte Elastase (Neutrophil Elastase)IBA
4. Pregnancy-Associated alpha 2-Macroglobulins (alpha 2 Macroglobulin)IBA
5. DNA (Deoxyribonucleic Acid)IBA
6. CopperIBA
7. Hepatitis B AntigensIBA
8. Peptide Hydrolases (Proteases)FDA Link
9. Peptides (Polypeptides)IBA
10. SmokeIBA

Therapies and Procedures

1. Therapeutics
2. Liver Transplantation
3. Self Administration (Administration, Self)
4. Lung Transplantation
5. Transplantation