A group of highly cellular primitive round cell neoplasms which occur extracranially in soft tissue and bone and are derived from embryonal neural crest cells. These tumors occur primarily in children and adolescents and share a number of characteristics with EWING SARCOMA.
Also Known As:
Peripheral Neuroectodermal Tumor; Peripheral Primitive Neuroectodermal Tumor; Neuroectodermal Tumors, Primitive, Peripheral; (pPNET) Peripheral Primitive Neuroectodermal Tumors; Extracranial Primitive Neuroectodermal Tumor; Neuroectodermal Neoplasm, Peripheral Primitive; Neuroectodermal Tumor, Peripheral Primitive; Neuroepithelioma, Peripheral; Peripheral Primitive Neuroectodermal Neoplasm; Primitive Neuroectodermal Tumor, Extracranial; Neuroectodermal Tumors, Peripheral; Neuroepitheliomas, Peripheral; Peripheral Neuroectodermal Tumors; Peripheral Neuroepithelioma; Peripheral Neuroepitheliomas; Tumor, Peripheral Neuroectodermal; Tumors, Peripheral Neuroectodermal; Neuroectodermal Tumor, Peripheral