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Central Pontine Myelinolysis

A demyelinating condition affecting the PONS and characterized clinically by an acute progressive QUADRIPLEGIA; DYSARTHRIA; DYSPHAGIA; and alterations of consciousness. Pathologic features include prominent demyelination in the central PONS with sparing of axons and neurons. This condition is usually associated with systemic disorders such as HYPONATREMIA; chronic ALCOHOLISM; LIVER FAILURE; severe BURNS; malignant NEOPLASMS; hemorrhagic PANCREATITIS; HEMODIALYSIS; and SEPSIS. The rapid medical correction of hyponatremia has been cited as a cause of this condition. (From Adams et al., Principles of Neurology, 6th ed, pp1125-6)
Also Known As:
Myelinolysis, Central Pontine; Extrapontine Myelinoclasis; Myelinoclasis, Central Pontine; Pontine Myelinolysis, Central; Central Pontine Myelinoclasis; Extrapontine Myelinoclases; Extrapontine Myelinolyses; Myelinoclases, Extrapontine; Myelinoclasis, Extrapontine; Myelinolyses, Extrapontine; Myelinolysis, Extrapontine; Extrapontine Myelinolysis
Networked: 253 relevant articles (6 outcomes, 5 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Hypernatremia
2. Cognitive Dysfunction
3. Psychogenic Polydipsia
4. Demyelinating Diseases (Demyelinating Disease)
5. Brain Edema (Cerebral Edema)

Experts

1. Yu, Jun: 4 articles (01/2006 - 06/2004)
2. Liang, Ting-bo: 3 articles (01/2006 - 06/2004)
3. Yoshida, Eric M: 2 articles (07/2019 - 12/2010)
4. Burra, Patrizia: 2 articles (06/2015 - 03/2009)
5. Senzolo, Marco: 2 articles (06/2015 - 03/2009)
6. Guo, Yong: 2 articles (07/2013 - 12/2006)
7. Deleu, Dirk: 2 articles (01/2012 - 10/2005)
8. Kim, Ki-Hun: 2 articles (01/2009 - 07/2007)
9. Lee, Sung-Gyu: 2 articles (01/2009 - 07/2007)
10. Wijdicks, Eelco F M: 2 articles (01/2009 - 07/2002)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Central Pontine Myelinolysis:
1. Intravenous Immunoglobulins (IVIG)FDA Link
2. Sodium Bicarbonate (Baking Soda)FDA LinkGeneric
3. Clozapine (Clozaril)FDA LinkGeneric
4. Zolpidem (Ambien)FDA LinkGeneric
5. ElectrolytesIBA
6. SodiumIBA
7. Vasopressins (Vasopressin)IBA
8. Cyclosporine (Ciclosporin)FDA LinkGeneric
9. Glucose (Dextrose)FDA LinkGeneric
10. Tacrolimus (Prograf)FDA LinkGeneric

Therapies and Procedures

1. Liver Transplantation
2. Therapeutics
3. Plasmapheresis
4. Highly Active Antiretroviral Therapy (HAART)
5. Plasma Exchange