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Bovine Spongiform Encephalopathy (Mad Cow Disease)

A transmissible spongiform encephalopathy of cattle associated with abnormal prion proteins in the brain. Affected animals develop excitability and salivation followed by ATAXIA. This disorder has been associated with consumption of SCRAPIE infected ruminant derived protein. This condition may be transmitted to humans, where it is referred to as variant or new variant CREUTZFELDT-JAKOB SYNDROME. (Vet Rec 1998 Jul 25;143(41):101-5)
Also Known As:
Mad Cow Disease; Encephalopathy, Bovine Spongiform; BSE (Bovine Spongiform Encephalopathy); Encephalitis, Bovine Spongiform; BSEs (Bovine Spongiform Encephalopathy); Bovine Spongiform Encephalitis; Mad Cow Diseases; Spongiform Encephalopathy, Bovine
Networked: 902 relevant articles (8 outcomes, 59 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Scrapie
2. Infections
3. Creutzfeldt-Jakob Syndrome (Creutzfeldt-Jakob Disease)
4. Chronic Wasting Disease
5. Kuru

Experts

1. Yokoyama, Takashi: 33 articles (01/2020 - 05/2002)
2. Collinge, John: 26 articles (12/2019 - 12/2002)
3. Masujin, Kentaro: 24 articles (01/2020 - 06/2007)
4. Okada, Hiroyuki: 21 articles (01/2020 - 09/2007)
5. Iwamaru, Yoshifumi: 20 articles (05/2022 - 05/2004)
6. Mohri, Shirou: 20 articles (01/2020 - 04/2007)
7. Baron, Thierry: 20 articles (10/2014 - 02/2003)
8. Imamura, Morikazu: 18 articles (05/2022 - 03/2005)
9. Matsuura, Yuichi: 18 articles (05/2022 - 07/2008)
10. Jeffrey, Martin: 16 articles (01/2021 - 05/2003)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Bovine Spongiform Encephalopathy:
1. PrionsIBA
2. Prion ProteinsIBA
3. Amyloid (Amyloid Fibrils)IBA
4. Sericins (Sericin)IBA
5. Heparin (Liquaemin)FDA LinkGeneric
6. ParaffinIBA
7. Formaldehyde (Formol)FDA Link
8. Biomarkers (Surrogate Marker)IBA
9. Aprotinin (Trasylol)FDA Link
10. Amyloidogenic ProteinsIBA

Therapies and Procedures

1. Blood Transfusion (Blood Transfusions)
2. Surgical Instruments (Clip)
3. Prostheses and Implants (Prosthesis)
4. Therapeutics
5. Operative Surgical Procedures