Designation for several severe forms of ichthyosis, present at birth, that are characterized by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalized scaling. The forms include bullous (HYPERKERATOSIS, EPIDERMOLYTIC), non-bullous (ICHTHYOSIS, LAMELLAR), wet type, and dry type.
Also Known As:
Ichthyosiform Erythroderma, Congenital; Congenital Ichthyosiform Erythroderma, Dry Type; Congenital Ichthyosiform Erythroderma, Wet Type; Erythroderma, Congenital Ichthyosiform; Congenital Ichthyosiform Erythrodermas; Erythrodermas, Congenital Ichthyosiform; Ichthyosiform Erythrodermas, Congenital